Primary Cilia in Cystic Kidney Disease (Q39242476)

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A Human Syndrome Caused by Immotile Cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Novel function of the ciliogenic transcription factor RFX3 in development of the endocrine pancreas

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

IFT27, encoding a small GTPase component of IFT particles, is mutated in a consanguineous family with Bardet-Biedl syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Differential regulation of node formation, nodal ciliogenesis and cilia positioning by Noto and Foxj1

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Basal body dysfunction is a likely cause of pleiotropic Bardet-Biedl syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Loss of GLIS2 causes nephronophthisis in humans and mice by increased apoptosis and fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Stages of ciliogenesis and regulation of ciliary length

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ciliary secretion: switching the cellular antenna to 'transmit'.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A chemical screen identifies class a g-protein coupled receptors as regulators of cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Actin is required for IFT regulation in Chlamydomonas reinhardtii

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

IFT80, which encodes a conserved intraflagellar transport protein, is mutated in Jeune asphyxiating thoracic dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Bardet-Biedl syndrome proteins are required for the localization of G protein-coupled receptors to primary cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

MIM and cortactin antagonism regulates ciliogenesis and hedgehog signaling.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Identification of signaling pathways regulating primary cilium length and flow-mediated adaptation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The WD repeat-containing protein IFTA-1 is required for retrograde intraflagellar transport.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The future of ciliary and flagellar membrane research

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia regulate mTORC1 activity and cell size through Lkb1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Usher syndrome type I associated with bronchiectasis and immotile nasal cilia in two brothers

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The bld1 mutation identifies the Chlamydomonas osm-6 homolog as a gene required for flagellar assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Regulation of cilium length and intraflagellar transport.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutations in IFT172 cause isolated retinal degeneration and Bardet-Biedl syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutation of the MAP kinase DYF-5 affects docking and undocking of kinesin-2 motors and reduces their speed in the cilia of Caenorhabditis elegans

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Altered trafficking and stability of polycystins underlie polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The genetics and physiology of polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Orpk mouse model of polycystic kidney disease reveals essential role of primary cilia in pancreatic tissue organization

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Corticosteroid-induced kidney dysmorphogenesis is associated with deregulated expression of known cystogenic molecules, as well as Indian hedgehog

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-1 surface localization is stimulated by polycystin-2 and cleavage at the G protein-coupled receptor proteolytic site

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanical stimuli induce cleavage and nuclear translocation of the polycystin-1 C terminus

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Modulation of Ciliary Phosphoinositide Content Regulates Trafficking and Sonic Hedgehog Signaling Output.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A ciliopathy complex at the transition zone protects the cilia as a privileged membrane domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-2 and phosphodiesterase 4C are components of a ciliary A-kinase anchoring protein complex that is disrupted in cystic kidney diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The ciliopathy-associated protein homologs RPGRIP1 and RPGRIP1L are linked to cilium integrity through interaction with Nek4 serine/threonine kinase.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Positional cloning of jcpk/bpk locus of the mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Chlamydomonas kinesin-II-dependent intraflagellar transport (IFT): IFT particles contain proteins required for ciliary assembly in Caenorhabditis elegans sensory neurons

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Compartmentalized calcium signaling in cilia regulates intraflagellar transport.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Vertebrate Smoothened functions at the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Kif3a constrains beta-catenin-dependent Wnt signalling through dual ciliary and non-ciliary mechanisms

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Tubulin transport by IFT is upregulated during ciliary growth by a cilium-autonomous mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TTC21B contributes both causal and modifying alleles across the ciliopathy spectrum

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Meckel-Gruber Syndrome proteins MKS1 and meckelin interact and are required for primary cilium formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Localization of intraflagellar transport protein IFT52 identifies basal body transitional fibers as the docking site for IFT particles

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Direct recording and molecular identification of the calcium channel of primary cilia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia are specialized calcium signalling organelles

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia are not calcium-responsive mechanosensors

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutations in LCA5, encoding the ciliary protein lebercilin, cause Leber congenital amaurosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A role for the membrane in regulating Chlamydomonas flagellar length

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cilia and developmental signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

IFT27 links the BBSome to IFT for maintenance of the ciliary signaling compartment.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intraflagellar transport particle size scales inversely with flagellar length: revisiting the balance-point length control model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Formation of primary cilia in the renal epithelium is regulated by the von Hippel-Lindau tumor suppressor protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The exocyst protein Sec10 interacts with Polycystin-2 and knockdown causes PKD-phenotypes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The intraflagellar transport protein IFT20 is associated with the Golgi complex and is required for cilia assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

PI3K class II α controls spatially restricted endosomal PtdIns3P and Rab11 activation to promote primary cilium function

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Phosphoinositide 3-Kinase-C2α Regulates Polycystin-2 Ciliary Entry and Protects against Kidney Cyst Formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Reduced ciliary polycystin-2 in induced pluripotent stem cells from polycystic kidney disease patients with PKD1 mutations

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-1 maturation requires polycystin-2 in a dose-dependent manner

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Biliary and pancreatic dysgenesis in mice harboring a mutation in Pkhd1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Genetic interaction studies link autosomal dominant and recessive polycystic kidney disease in a common pathway.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A transition zone complex regulates mammalian ciliogenesis and ciliary membrane composition

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Phosphoinositides Regulate Ciliary Protein Trafficking to Modulate Hedgehog Signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-2 traffics to cilia independently of polycystin-1 by using an N-terminal RVxP motif

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The BBSome Controls Energy Homeostasis by Mediating the Transport of the Leptin Receptor to the Plasma Membrane

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Unilateral nephrectomy elongates primary cilia in the remaining kidney via reactive oxygen species.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Leptin-promoted cilia assembly is critical for normal energy balance

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The tuberous sclerosis proteins regulate formation of the primary cilium via a rapamycin-insensitive and polycystin 1-independent pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

IP3 signaling is required for cilia formation and left-right body axis determination in Xenopus embryos.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Gli2 and Gli3 localize to cilia and require the intraflagellar transport protein polaris for processing and function

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Identification of CHE-13, a novel intraflagellar transport protein required for cilia formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The kinesin-4 protein Kif7 regulates mammalian Hedgehog signalling by organizing the cilium tip compartment

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Subcellular localization of ALMS1 supports involvement of centrosome and basal body dysfunction in the pathogenesis of obesity, insulin resistance, and type 2 diabetes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutations in C8ORF37 cause Bardet Biedl syndrome (BBS21)

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The kinases LF4 and CNK2 control ciliary length by feedback regulation of assembly and disassembly rates.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-2 takes different routes to the somatic and ciliary plasma membrane

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Characterization of PKD protein-positive exosome-like vesicles

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Retinitis pigmentosa GTPase regulator (RPGRr)-interacting protein is stably associated with the photoreceptor ciliary axoneme and anchors RPGR to the connecting cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Tolvaptan plus pasireotide shows enhanced efficacy in a PKD1 model

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Functional polycystin-1 dosage governs autosomal dominant polycystic kidney disease severity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Trafficking in and to the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

STAM and Hrs down-regulate ciliary TRP receptors

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cilia and Hedgehog responsiveness in the mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Hedgehog signalling in the mouse requires intraflagellar transport proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Reduction of ciliary length through pharmacologic or genetic inhibition of CDK5 attenuates polycystic kidney disease in a model of nephronophthisis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

mTOR signaling in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanisms and functions of Hedgehog signalling across the metazoa

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Protein particles in Chlamydomonas flagella undergo a transport cycle consisting of four phases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Retrograde intraflagellar transport mutants identify complex A proteins with multiple genetic interactions in Chlamydomonas reinhardtii

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

INPP5E mutations cause primary cilium signaling defects, ciliary instability and ciliopathies in human and mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cilioplasm is a cellular compartment for calcium signaling in response to mechanical and chemical stimuli

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

L-type calcium channel modulates cystic kidney phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Deletion of IFT20 in the mouse kidney causes misorientation of the mitotic spindle and cystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Disruption of IFT complex A causes cystic kidneys without mitotic spindle misorientation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

IFT25 links the signal-dependent movement of Hedgehog components to intraflagellar transport

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cellular Mechanisms of Ciliary Length Control

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Genetics of human Bardet-Biedl syndrome, an updates

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia mechanics affects cell mechanosensation: A computational study.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Genome-wide screen identifies novel machineries required for both ciliogenesis and cell cycle arrest upon serum starvation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Nek2 activation of Kif24 ensures cilium disassembly during the cell cycle

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Functional genomic screen for modulators of ciliogenesis and cilium length

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The polycystin complex mediates Wnt/Ca(2+) signalling.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ciliary membrane proteins traffic through the Golgi via a Rabep1/GGA1/Arl3-dependent mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Coordination of Rab8 and Rab11 in primary ciliogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TRPP2 and TRPV4 form a polymodal sensory channel complex

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Chlamydomonas kinesin-like protein FLA10 is involved in motility associated with the flagellar membrane

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A motility in the eukaryotic flagellum unrelated to flagellar beating

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Novel functional complexity of polycystin-1 by GPS cleavage in vivo: role in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-1 C-terminal tail associates with beta-catenin and inhibits canonical Wnt signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Impaired Wnt-beta-catenin signaling disrupts adult renal homeostasis and leads to cystic kidney ciliopathy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Chlamydomonas reinhardtii BBSome is an IFT cargo required for export of specific signaling proteins from flagella

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Meckel syndrome protein meckelin (TMEM67) is a key regulator of cilia function but is not required for tissue planar polarity.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Increased hedgehog signaling in postnatal kidney results in aberrant activation of nephron developmental programs

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The intraflagellar transport protein IFT27 promotes BBSome exit from cilia through the GTPase ARL6/BBS3.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Kidney-specific inactivation of the KIF3A subunit of kinesin-II inhibits renal ciliogenesis and produces polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Recurrent CNVs and SNVs at the NPHP1 locus contribute pathogenic alleles to Bardet-Biedl syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanoregulation of intracellular Ca2+ concentration is attenuated in collecting duct of monocilium-impaired orpk mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mouse intraflagellar transport proteins regulate both the activator and repressor functions of Gli transcription factors

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Effect of flow and stretch on the [Ca2+]i response of principal and intercalated cells in cortical collecting duct

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Genetic basis of Joubert syndrome and related disorders of cerebellar development

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-1, STAT6, and P100 function in a pathway that transduces ciliary mechanosensation and is activated in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Avalanche-like behavior in ciliary import.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Birt-Hogg-Dube syndrome is a novel ciliopathy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Evidence of a role of inositol polyphosphate 5-phosphatase INPP5E in cilia formation in zebrafish

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Loss of cilia suppresses cyst growth in genetic models of autosomal dominant polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Loss of the ciliary kinase Nek8 causes left-right asymmetry defects

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Transient ciliogenesis involving Bardet-Biedl syndrome proteins is a fundamental characteristic of adipogenic differentiation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Exome sequencing identifies mutations in LZTFL1, a BBSome and smoothened trafficking regulator, in a family with Bardet--Biedl syndrome with situs inversus and insertional polydactyly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intraflagellar transport balances continuous turnover of outer doublet microtubules: implications for flagellar length control

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Flagellar length control system: testing a simple model based on intraflagellar transport and turnover

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cholangiocyte primary cilia in liver health and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Divalent interaction of the GGAs with the Rabaptin-5-Rabex-5 complex

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ciliary targeting motif VxPx directs assembly of a trafficking module through Arf4.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The γ-secretase cleavage product of polycystin-1 regulates TCF and CHOP-mediated transcriptional activation through a p300-dependent mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Proteomics of Primary Cilia by Proximity Labeling

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

T-cell factor/β-catenin activity is suppressed in two different models of autosomal dominant polycystic kidney disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The evolution of eukaryotic cilia and flagella as motile and sensory organelles

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TULP3 bridges the IFT-A complex and membrane phosphoinositides to promote trafficking of G protein-coupled receptors into primary cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A core complex of BBS proteins cooperates with the GTPase Rab8 to promote ciliary membrane biogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Fluid flow and interlinked feedback loops establish left-right asymmetric decay of Cerl2 mRNA.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Inhibition of glucosylceramide accumulation results in effective blockade of polycystic kidney disease in mouse models

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystins 1 and 2 mediate mechanosensation in the primary cilium of kidney cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Gli protein activity is controlled by multisite phosphorylation in vertebrate Hedgehog signaling.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Hedgehog signaling from the primary cilium to the nucleus: an emerging picture of ciliary localization, trafficking and transduction

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

An inducible CiliaGFP mouse model for in vivo visualization and analysis of cilia in live tissue.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Context-dependent regulation of Wnt signaling through the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Regulation of primary cilia formation and left-right patterning in zebrafish by a noncanonical Wnt signaling mediator, duboraya

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Signal transducer and activator of transcription-6 (STAT6) inhibition suppresses renal cyst growth in polycystic kidney disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Nephrocystin-5, a ciliary IQ domain protein, is mutated in Senior-Loken syndrome and interacts with RPGR and calmodulin

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutations in INVS encoding inversin cause nephronophthisis type 2, linking renal cystic disease to the function of primary cilia and left-right axis determination

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Adenylate cyclase regulates elongation of mammalian primary cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Osmolar regulation of endothelin-1 production by the inner medullary collecting duct

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Chlamydomonas fla mutants reveal a link between deflagellation and intraflagellar transport

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Chlamydomonas IFT88 and its mouse homologue, polycystic kidney disease gene tg737, are required for assembly of cilia and flagella

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The DHC1b (DHC2) isoform of cytoplasmic dynein is required for flagellar assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A dynein light chain is essential for the retrograde particle movement of intraflagellar transport (IFT)

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Chlamydomonas IFT172 is encoded by FLA11, interacts with CrEB1, and regulates IFT at the flagellar tip.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutant sensory cilia in the nematode Caenorhabditis elegans

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Glycosphingolipid synthesis is essential for MDCK cell differentiation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A microtubule depolymerizing kinesin functions during both flagellar disassembly and flagellar assembly in Chlamydomonas

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A critical developmental switch defines the kinetics of kidney cyst formation after loss of Pkd1

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Analysis of the morphology and function of primary cilia in connective tissues: a cellular cybernetic probe?

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mutations in GANAB, Encoding the Glucosidase IIα Subunit, Cause Autosomal-Dominant Polycystic Kidney and Liver Disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cytoplasmic dynein heavy chain 1b is required for flagellar assembly in Chlamydomonas

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Bending the MDCK cell primary cilium increases intracellular calcium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Removal of the MDCK cell primary cilium abolishes flow sensing

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

HEF1-dependent Aurora A activation induces disassembly of the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cystic renal neoplasia following conditional inactivation of apc in mouse renal tubular epithelium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intraflagellar transport protein 122 antagonizes Sonic Hedgehog signaling and controls ciliary localization of pathway components

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

c-Met and NF-κB-dependent overexpression of Wnt7a and -7b and Pax2 promotes cystogenesis in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Failure to ubiquitinate c-Met leads to hyperactivation of mTOR signaling in a mouse model of autosomal dominant polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intraflagellar transport protein 27 is a small G protein involved in cell-cycle control

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Modeling ciliopathies: Primary cilia in development and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

An mTOR kinase inhibitor slows disease progression in a rat model of polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Patched1 regulates hedgehog signaling at the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

OFD1 is a centrosomal/basal body protein expressed during mesenchymal-epithelial transition in human nephrogenesis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Flagellar regeneration in protozoan flagellates

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

21 January 2018

Intraflagellar transport

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Effect of Sirolimus on Disease Progression in Patients with Autosomal Dominant Polycystic Kidney Disease and CKD Stages 3b-4.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ellis-van Creveld syndrome and Weyers acrodental dysostosis are caused by cilia-mediated diminished response to hedgehog ligands

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanical properties of primary cilia regulate the response to fluid flow

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ciliogenesis in normal human kidney development and post-natal life

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Identification of a novel mutation confirms the implication of IFT172 (BBS20) in Bardet-Biedl syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Exome sequencing of Bardet-Biedl syndrome patient identifies a null mutation in the BBSome subunit BBIP1 (BBS18)

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Arl3 and RP2 mediated assembly and traffic of membrane associated cilia proteins.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

BBS6, BBS10, and BBS12 form a complex with CCT/TRiC family chaperonins and mediate BBSome assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A novel protein LZTFL1 regulates ciliary trafficking of the BBSome and Smoothened

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Sirolimus and kidney growth in autosomal dominant polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia modulate Ihh signal transduction in response to hydrostatic loading of growth plate chondrocytes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Soluble levels of cytosolic tubulin regulate ciliary length control

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Folate-conjugated rapamycin slows progression of polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The mTOR pathway is regulated by polycystin-1, and its inhibition reverses renal cystogenesis in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Role of a class DHC1b dynein in retrograde transport of IFT motors and IFT raft particles along cilia, but not dendrites, in chemosensory neurons of living Caenorhabditis elegans

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Inversin, the gene product mutated in nephronophthisis type II, functions as a molecular switch between Wnt signaling pathways

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Loss of primary cilia results in deregulated and unabated apical calcium entry in ARPKD collecting duct cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Development of polycystic kidney disease in juvenile cystic kidney mice: insights into pathogenesis, ciliary abnormalities, and common features with human disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Flagellar protein dynamics in Chlamydomonas

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Systems biology of autosomal dominant polycystic kidney disease (ADPKD): computational identification of gene expression pathways and integrated regulatory networks

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Centrioles and the formation of rudimentary cilia by fibroblasts and smooth muscle cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Nek2 localises to the distal portion of the mother centriole/basal body and is required for timely cilium disassembly at the G2/M transition.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Synthesis and Turnover of Embryonic Sea Urchin Ciliary Proteins during Selective Inhibition of Tubulin Synthesis and Assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ttc21b is required to restrict sonic hedgehog activity in the developing mouse forebrain

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Bardet-Biedl syndrome proteins 1 and 3 regulate the ciliary trafficking of polycystic kidney disease 1 protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Genetically encoded calcium indicator illuminates calcium dynamics in primary cilia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Regulation of polycystin-1 ciliary trafficking by motifs at its C-terminus and polycystin-2 but not by cleavage at the GPS site

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The canonical Wnt signaling pathway is not involved in renal cyst development in the kidneys of inv mutant mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A genetic screen in zebrafish identifies cilia genes as a principal cause of cystic kidney

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Pyrimethamine inhibits adult polycystic kidney disease by modulating STAT signaling pathways

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Activating AMP-activated protein kinase (AMPK) slows renal cystogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystin-1 regulates STAT activity by a dual mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The cleaved cytoplasmic tail of polycystin-1 regulates Src-dependent STAT3 activation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

CDKL5 regulates flagellar length and localizes to the base of the flagella in Chlamydomonas

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Glycogen synthase kinase-3β promotes cyst expansion in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Rapamycin markedly slows disease progression in a rat model of polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

NEK1 mutations cause short-rib polydactyly syndrome type majewski

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia disassembly down-regulates mechanosensitive hedgehog signalling: a feedback mechanism controlling ADAMTS-5 expression in chondrocytes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanisms of Disease: autosomal dominant and recessive polycystic kidney diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Tolvaptan in Patients with Autosomal Dominant Polycystic Kidney Disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

An age of enlightenment for cilia: The FASEB summer research conference on the "Biology of Cilia and Flagella"

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Developmental signaling: does it bridge the gap between cilia dysfunction and renal cystogenesis?

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Downregulating hedgehog signaling reduces renal cystogenic potential of mouse models

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

THM1 negatively modulates mouse sonic hedgehog signal transduction and affects retrograde intraflagellar transport in cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The RNA-binding protein bicaudal C regulates polycystin 2 in the kidney by antagonizing miR-17 activity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Role of G-Protein-Coupled Receptor Proteolysis Site Cleavage of Polycystin-1 in Renal Physiology and Polycystic Kidney Disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Roles of dopamine receptor on chemosensory and mechanosensory primary cilia in renal epithelial cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

DLK-1/p38 MAP Kinase Signaling Controls Cilium Length by Regulating RAB-5 Mediated Endocytosis in Caenorhabditis elegans

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Renal primary cilia lengthen after acute tubular necrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Inhibition of mTOR with sirolimus slows disease progression in Han:SPRD rats with autosomal dominant polycystic kidney disease (ADPKD).

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cranioectodermal Dysplasia, Sensenbrenner syndrome, is a ciliopathy caused by mutations in the IFT122 gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cyclic AMP-mediated cyst expansion

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Everolimus in patients with autosomal dominant polycystic kidney disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Effectiveness of vasopressin V2 receptor antagonists OPC-31260 and OPC-41061 on polycystic kidney disease development in the PCK rat.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Aquaporin-1 retards renal cyst development in polycystic kidney disease by inhibition of Wnt signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

C. elegans ciliated sensory neurons release extracellular vesicles that function in animal communication

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Vasopressin directly regulates cyst growth in polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Fibrocystin/polyductin, found in the same protein complex with polycystin-2, regulates calcium responses in kidney epithelia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A conserved signal and GTPase complex are required for the ciliary transport of polycystin-1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Characterization of cis-autoproteolysis of polycystin-1, the product of human polycystic kidney disease 1 gene.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystic kidney disease and renal injury repair: common pathways, fluid flow, and the function of polycystin-1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Primary cilia membrane assembly is initiated by Rab11 and transport protein particle II (TRAPPII) complex-dependent trafficking of Rabin8 to the centrosome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Aberrant Wnt signalling and cellular over-proliferation in a novel mouse model of Meckel-Gruber syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The NIMA-family kinase, Nek1 affects the stability of centrosomes and ciliogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

MKS and NPHP modules cooperate to establish basal body/transition zone membrane associations and ciliary gate function during ciliogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Members of the NIMA-related kinase family promote disassembly of cilia by multiple mechanisms

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Ciliary ectosomes: transmissions from the cell's antenna

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The cilium secretes bioactive ectosomes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A mouse model of autosomal recessive polycystic kidney disease with biliary duct and proximal tubule dilatation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

An ARL3-UNC119-RP2 GTPase cycle targets myristoylated NPHP3 to the primary cilium

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

BBS4 and BBS5 show functional redundancy in the BBSome to regulate the degradative sorting of ciliary sensory receptors

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Renal accumulation and excretion of cyclic adenosine monophosphate in a murine model of slowly progressive polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Calcium restriction allows cAMP activation of the B-Raf/ERK pathway, switching cells to a cAMP-dependent growth-stimulated phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Superresolution Pattern Recognition Reveals the Architectural Map of the Ciliary Transition Zone

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Modulation of Polycystic Kidney Disease Severity by Phosphodiesterase 1 and 3 Subfamilies

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Centrin 2 is required for mouse olfactory ciliary trafficking and development of ependymal cilia planar polarity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The polycystic kidney disease proteins, polycystin-1, polycystin-2, polaris, and cystin, are co-localized in renal cilia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The renewal of rod and cone outer segments in the rhesus monkey

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Participation of the retinal pigment epithelium in the rod outer segment renewal process

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intraciliary calcium oscillations initiate vertebrate left-right asymmetry

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TRPV4 dysfunction promotes renal cystogenesis in autosomal recessive polycystic kidney disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TRPP2 and TRPV4 form an EGF-activated calcium permeable channel at the apical membrane of renal collecting duct cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Bardet-Biedl syndrome 3 (Bbs3) knockout mouse model reveals common BBS-associated phenotypes and Bbs3 unique phenotypes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Intrinsic protein-protein interaction-mediated and chaperonin-assisted sequential assembly of stable bardet-biedl syndrome protein complex, the BBSome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Polycystins and primary cilia: primers for cell cycle progression

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The Small GTPase Cdc42 Is Necessary for Primary Ciliogenesis in Renal Tubular Epithelial Cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

The exocyst protein Sec10 is necessary for primary ciliogenesis and cystogenesis in vitro

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A mouse model for cystic biliary dysgenesis in autosomal recessive polycystic kidney disease (ARPKD)

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Mechanisms regulating cilia growth and cilia function in endothelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

A novel MAP kinase regulates flagellar length in Chlamydomonas

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Strategies to inhibit cyst formation in ADPKD

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Cell signaling. A ciliary signaling switch

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Inhibition of renal cystic disease development and progression by a vasopressin V2 receptor antagonist

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

TTC26/DYF13 is an intraflagellar transport protein required for transport of motility-related proteins into flagella

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Subcellular spatial regulation of canonical Wnt signalling at the primary cilium

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Erratum: Early steps in primary cilium assembly require EHD1/EHD3-dependent ciliary vesicle formation

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Pkd1 and Nek8 mutations affect cell-cell adhesion and cilia in cysts formed in kidney organ cultures

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Early development of polycystic kidney disease in transgenic mice expressing an activated mutant of the beta-catenin gene

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Dido3-dependent HDAC6 targeting controls cilium size.

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Rationale and Design of the TEMPO (Tolvaptan Efficacy and Safety in Management of Autosomal Dominant Polycystic Kidney Disease and Its Outcomes) 3-4 Study

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Effective treatment of an orthologous model of autosomal dominant polycystic kidney disease

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Renal cilia display length alterations following tubular injury and are present early in epithelial repair

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Calcium restores a normal proliferation phenotype in human polycystic kidney disease epithelial cells

31 March 2020

1 reference

https://api.crossref.org/works/10.1007%2F978-3-319-51436-9_11

Evidence of congenitally nonfunctioning cilia in the tracheobronchial tract in two subjects

31 March 2020

1 reference

12 December 2020

Molecular basis of the obesity associated with Bardet-Biedl syndrome

1 reference

12 December 2020

A novel WD40 protein, CHE-2, acts cell-autonomously in the formation of C. elegans sensory cilia.

1 reference

12 December 2020

Tendon cell ciliary length as a biomarker of in situ cytoskeletal tensional homeostasis

1 reference

12 December 2020

A polycystic kidney-disease gene homologue required for male mating behaviour in C. elegans

1 reference

12 December 2020