From Charcot to SOD1: mechanisms of selective motor neuron death in ALS. (Q33792977)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10595505%20AND%20SRC:MED&resulttype=core&format=json

2 November 2019

review article

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title

From Charcot to SOD1: mechanisms of selective motor neuron death in ALS (English)

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10595505%20AND%20SRC:MED&resulttype=core&format=json

amyotrophic lateral sclerosis

2 November 2019

main subject

1 reference

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10595505%20AND%20SRC:MED&resulttype=core&format=json

2 November 2019

D W Cleveland

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29 July 2017

language of work or name

English

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publication date

1 November 1999

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2 November 2019

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2 November 2019

volume

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2 November 2019

issue

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2 November 2019

page(s)

515-520

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Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis

2 November 2019

cites work

1 reference

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7 January 2021

Protein oxidative damage in a transgenic mouse model of familial amyotrophic lateral sclerosis

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7 January 2021

ALS, SOD and peroxynitrite

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7 January 2021

Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity

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7 January 2021

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

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7 January 2021

Amyotrophic lateral sclerosis: recent insights from genetics and transgenic mice

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7 January 2021

Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

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7 January 2021

Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superox

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7 January 2021

ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

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7 January 2021

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

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7 January 2021

Chaperone-facilitated copper binding is a property common to several classes of familial amyotrophic lateral sclerosis-linked superoxide dismutase mutants

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7 January 2021

Protective effect of neurofilament heavy gene overexpression in motor neuron disease induced by mutant superoxide dismutase

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7 January 2021

Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis

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7 January 2021

The copper chaperone for superoxide dismutase

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7 January 2021

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

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7 January 2021

Evidence of increased oxidative damage in both sporadic and familial amyotrophic lateral sclerosis

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7 January 2021

Variants of the heavy neurofilament subunit are associated with the development of amyotrophic lateral sclerosis

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7 January 2021

Inhibition of ICE slows ALS in mice

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7 January 2021

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

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7 January 2021

Benefit of vitamin E, riluzole, and gabapentin in a transgenic model of familial amyotrophic lateral sclerosis

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7 January 2021

Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis

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7 January 2021

Morphometric Comparison of the Vulnerability of Peripheral Motor and Sensory Neurons in Amyotrophic Lateral Sclerosis

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7 January 2021

Neuroprotective effects of creatine in a transgenic animal model of amyotrophic lateral sclerosis.

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7 January 2021

Bcl-2: prolonging life in a transgenic mouse model of familial amyotrophic lateral sclerosis

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7 January 2021

Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II

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7 January 2021

Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis

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7 January 2021

Identification of alternative splicing forms of GLT-1 mRNA in the spinal cord of amyotrophic lateral sclerosis patients

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7 January 2021

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

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7 January 2021

Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

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7 January 2021

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

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7 January 2021

Selective loss of glial glutamate transporter GLT‐1 in amyotrophic lateral sclerosis

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7 January 2021

Reexamination of the mechanism of hydroxyl radical adducts formed from the reaction between familial amyotrophic lateral sclerosis-associated Cu,Zn superoxide dismutase mutants and H2O2.

1 reference

https://api.crossref.org/works/10.1016%2FS0896-6273%2800%2981108-3

7 January 2021

Novel insertion in the KSP region of the neurofilament heavy gene in amyotrophic lateral sclerosis (ALS)

1 reference

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7 January 2021

SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter

1 reference

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7 January 2021

Selective impairment of fast anterograde axonal transport in the peripheral nerves of asymptomatic transgenic mice with a G93A mutant SOD1 gene

1 reference

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7 January 2021

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

1 reference

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7 January 2021

Slowing of axonal transport is a very early event in the toxicity of ALS-linked SOD1 mutants to motor neurons

1 reference

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7 January 2021

Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant

1 reference

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7 January 2021

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

1 reference

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7 January 2021

10.1016/S0896-6273(00)81108-3

Identifiers

DOI

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10595505%20AND%20SRC:MED&resulttype=core&format=json

2 November 2019

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10595505%20AND%20SRC:MED&resulttype=core&format=json