Amyotrophic lateral sclerosis. unfolding the toxicity of the misfolded (Q34175381)

31 July 2017

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title

Amyotrophic lateral sclerosis. unfolding the toxicity of the misfolded (English)

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amyotrophic lateral sclerosis

31 July 2017

main subject

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J P Julien

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31 July 2017

language of work or name

English

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publication date

1 February 2001

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31 July 2017

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31 July 2017

volume

104

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31 July 2017

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31 July 2017

page(s)

581-591

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Glutamate slows axonal transport of neurofilaments in transfected neurons

31 July 2017

cites work

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Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis

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Inducible nitric oxide synthase up-regulation in a transgenic mouse model of familial amyotrophic lateral sclerosis

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7 January 2021

Partial deficiency of manganese superoxide dismutase exacerbates a transgenic mouse model of amyotrophic lateral sclerosis

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7 January 2021

Mutations in the glutamate transporter EAAT2 gene do not cause abnormal EAAT2 transcripts in amyotrophic lateral sclerosis

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7 January 2021

Increased motoneuron survival and improved neuromuscular function in transgenic ALS mice after intraspinal injection of an adeno-associated virus encoding Bcl-2.

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7 January 2021

Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis

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7 January 2021

Late onset of motor neurons in mice overexpressing wild-type peripherin

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7 January 2021

Formation of intermediate filament protein aggregates with disparate effects in two transgenic mouse models lacking the neurofilament light subunit

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7 January 2021

ALS, SOD and peroxynitrite

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7 January 2021

Detection and cellular localization of enterovirus RNA sequences in spinal cord of patients with ALS

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7 January 2021

Elevated "hydroxyl radical" generation in vivo in an animal model of amyotrophic lateral sclerosis.

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7 January 2021

Mitochondrial enzyme activity in amyotrophic lateral sclerosis: implications for the role of mitochondria in neuronal cell death

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7 January 2021

Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superox

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7 January 2021

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

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7 January 2021

Linkage of the gene for an autosomal dominant form of juvenile amyotrophic lateral sclerosis to chromosome 9q34.

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7 January 2021

From Charcot to SOD1: mechanisms of selective motor neuron death in ALS.

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7 January 2021

Amyotrophic Lateral Sclerosis Immunoglobulins Increase Intracellular Calcium in a Motoneuron Cell Line

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7 January 2021

Peripherin and neurofilament protein coexist in spinal spheroids of motor neuron disease

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7 January 2021

Protective effect of neurofilament heavy gene overexpression in motor neuron disease induced by mutant superoxide dismutase

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7 January 2021

Extra axonal neurofilaments do not exacerbate disease caused by mutant Cu,Zn superoxide dismutase.

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7 January 2021

Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis

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7 January 2021

Differential screening of mutated SOD1 transgenic mice reveals early up-regulation of a fast axonal transport component in spinal cord motor neurons

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7 January 2021

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

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7 January 2021

Human umbilical cord blood effect on sod mice (amyotrophic lateral sclerosis)

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7 January 2021

Induction of nitric oxide-dependent apoptosis in motor neurons by zinc-deficient superoxide dismutase

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7 January 2021

Pathogenesis of two axonopathies does not require axonal neurofilaments.

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7 January 2021

Lack of involvement of neuronal nitric oxide synthase in the pathogenesis of a transgenic mouse model of familial amyotrophic lateral sclerosis.

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7 January 2021

Evidence of Increased Oxidative Damage in Both Sporadic and Familial Amyotrophic Lateral Sclerosis

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7 January 2021

Variants of the heavy neurofilament subunit are associated with the development of amyotrophic lateral sclerosis

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7 January 2021

Expression of a dominant negative mutant of interleukin-1 beta converting enzyme in transgenic mice prevents neuronal cell death induced by trophic factor withdrawal and ischemic brain injury

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7 January 2021

Restricted expression of G86R Cu/Zn superoxide dismutase in astrocytes results in astrocytosis but does not cause motoneuron degeneration

1 reference

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7 January 2021

Benefit of vitamin E, riluzole, and gabapentin in a transgenic model of familial amyotrophic lateral sclerosis

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7 January 2021

Linkage of recessive familial amyotrophic lateral sclerosis to chromosome 2q33-q35.

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7 January 2021

Linkage of a commoner form of recessive amyotrophic lateral sclerosis to chromosome 15q15-q22 markers

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7 January 2021

Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis

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7 January 2021

Linkage of familial amyotrophic lateral sclerosis with frontotemporal dementia to chromosome 9q21-q22

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7 January 2021

Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

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7 January 2021

Chronic mitochondrial inhibition induces selective motoneuron death in vitro: a new model for amyotrophic lateral sclerosis

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7 January 2021

Neuroprotective effects of creatine in a transgenic animal model of amyotrophic lateral sclerosis.

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7 January 2021

Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

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7 January 2021

Overexpression of neurofilament subunit NF-L and NF-H extends survival of a mouse model for amyotrophic lateral sclerosis

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7 January 2021

Bcl-2: Prolonging Life in a Transgenic Mouse Model of Familial Amyotrophic Lateral Sclerosis

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7 January 2021

Altered ionic conductances in axons of transgenic mouse expressing the human neurofilament heavy gene: A mouse model of amyotrophic lateral sclerosis

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7 January 2021

Absence of p53: no effect in a transgenic mouse model of familial amyotrophic lateral sclerosis

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7 January 2021

A mutant neurofilament subunit causes massive, selective motor neuron death: implications for the pathogenesis of human motor neuron disease

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7 January 2021

Astrocytes interact intimately with degenerating motor neurons in mouse amyotrophic lateral sclerosis (ALS)

1 reference

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7 January 2021

Functional Role of Caspase-1 and Caspase-3 in an ALS Transgenic Mouse Model

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7 January 2021

Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis

1 reference

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7 January 2021

Neuronal death in amyotrophic lateral sclerosis is apoptosis: possible contribution of a programmed cell death mechanism

1 reference

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7 January 2021

Extra neurofilament NF-L subunits rescue motor neuron disease caused by overexpression of the human NF-H gene in mice.

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

A new variant of Charcot-Marie-Tooth disease type 2 is probably the result of a mutation in the neurofilament-light gene

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

The RNA of the glutamate transporter EAAT2 is variably spliced in amyotrophic lateral sclerosis and normal individuals

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Lack of apoptosis in mice with ALS

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7 January 2021

Reduction of axonal caliber does not alleviate motor neuron disease caused by mutant superoxide dismutase 1

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Caspase-1 is activated in neural cells and tissue with amyotrophic lateral sclerosis-associated mutations in copper-zinc superoxide dismutase.

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Caspase-1 and -3 are sequentially activated in motor neuron death in Cu,Zn superoxide dismutase-mediated familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

The prostate apoptosis response-4 protein participates in motor neuron degeneration in amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Selective loss of glial glutamate transporter GLT‐1 in amyotrophic lateral sclerosis

1 reference

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7 January 2021

Intracellular calcium parallels motoneuron degeneration in SOD-1 mutant mice.

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Nitration of the low molecular weight neurofilament is equivalent in sporadic amyotrophic lateral sclerosis and control cervical spinal cord

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Amyotrophic lateral sclerosis-linked glutamate transporter mutant has impaired glutamate clearance capacity

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Bax and Bcl-2 interaction in a transgenic mouse model of familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Toxicity of ALS-linked SOD1 mutants

1 reference

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7 January 2021

Copper chaperone for superoxide dismutase is essential to activate mammalian Cu/Zn superoxide dismutase

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

Characterization of neuronal intermediate filament protein expression in cervical spinal motor neurons in sporadic amyotrophic lateral sclerosis (ALS).

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

In vitro induction of neuronal apoptosis by anti-Fas antibody-containing sera from amyotrophic lateral sclerosis patients.

1 reference

https://api.crossref.org/works/10.1016%2FS0092-8674%2801%2900244-6

7 January 2021

10.1016/S0092-8674(01)00244-6

Identifiers

DOI

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31 July 2017

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