Stimulation of reactive oxygen species generation by disease-causing mutations of lipoamide dehydrogenase (Q57539864)

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Mitochondrial alpha-ketoglutarate dehydrogenase complex generates reactive oxygen species.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

alpha-Ketoglutarate dehydrogenase contributes to production of reactive oxygen species in glutamate-stimulated hippocampal neurons in situ

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Dihydrolipoyl dehydrogenase as a source of reactive oxygen species inhibited by caloric restriction and involved in Saccharomyces cerevisiae aging.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Oxidative alpha-ketoglutarate dehydrogenase inhibition via subtle elevations in monoamine oxidase B levels results in loss of spare respiratory capacity: implications for Parkinson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Modulation of mitochondrial function by hydrogen peroxide

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Inactivation of the 2-oxo acid dehydrogenase complexes upon generation of intrinsic radical species

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

The composition of the ketoglutarate dehydrogenase complex

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Cause and consequence: mitochondrial dysfunction initiates and propagates neuronal dysfunction, neuronal death and behavioral abnormalities in age-associated neurodegenerative diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Inhibition of the alpha-ketoglutarate dehydrogenase-mediated reactive oxygen species generation by lipoic acid.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Zinc is a potent inhibitor of thiol oxidoreductase activity and stimulates reactive oxygen species production by lipoamide dehydrogenase.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Intermediates in the catalytic action of lipoyl dehydrogenase (diaphorase)

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Crystal structure of human dihydrolipoamide dehydrogenase: NAD+/NADH binding and the structural basis of disease-causing mutations

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

pH-dependent substrate preference of pig heart lipoamide dehydrogenase varies with oligomeric state: response to mitochondrial matrix acidification

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Cryptic proteolytic activity of dihydrolipoamide dehydrogenase

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Leigh syndrome due to compound heterozygosity of dihydrolipoamide dehydrogenase gene mutations. Description of the first E3 splice site mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Identification of a common mutation (Gly194Cys) in both Arab Moslem and Ashkenazi Jewish patients with dihydrolipoamide dehydrogenase (E3) deficiency: possible beneficial effect of vitamin therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Identification of two missense mutations in a dihydrolipoamide dehydrogenase-deficient patient

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

A novel mutation in the dihydrolipoamide dehydrogenase E3 subunit gene (DLD) resulting in an atypical form of alpha-ketoglutarate dehydrogenase deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

The role of N286 and D320 in the reaction mechanism of human dihydrolipoamide dehydrogenase (E3) center domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Mechanisms of generation of oxygen radicals and reductive mobilization of ferritin iron by lipoamide dehydrogenase

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Spectroscopic studies of the characterization of recombinant human dihydrolipoamide dehydrogenase and its site-directed mutants.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Electrospray: from ions in solution to ions in the gas phase, what we know now.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Dihydrolipoyl dehydrogenase deficiency: a therapeutic trial with branched-chain amino acid restriction.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Structural basis of the dysfunctioning of human 2-oxo acid dehydrogenase complexes

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Periplasmic cold expression and one-step purification of human dihydrolipoamide dehydrogenase

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Refolding of the human dihydrolipoamide dehydrogenase

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

A new method for preparing flavin-adenine dinucleotide

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202

Oligomerization of nitrophorins

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDR202