Brazilian guidelines for the diagnosis and treatment of cystic fibrosis. (Q43538692)

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26 March 2020

title

Brazilian guidelines for the diagnosis and treatment of cystic fibrosis (English)

1 reference

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26 March 2020

0 references

Luiz Vicente Ribeiro Ferreira da Silva Filho

1 reference

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26 March 2020

Alberto Andrade Vergara

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26 March 2020

Antônio Fernando Ribeiro

1 reference

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26 March 2020

Carlos Antônio Riedi

1 reference

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26 March 2020

Elenara da Fonseca Andrade Procianoy

1 reference

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26 March 2020

Fabíola Villac Adde

1 reference

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26 March 2020

Francisco José Caldeira Reis

1 reference

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26 March 2020

José Dirceu Ribeiro

1 reference

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26 March 2020

Lídia Alice Torres

1 reference

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26 March 2020

Marcelo Bicalho de Fuccio

1 reference

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26 March 2020

Mônica de Cássia Firmida

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26 March 2020

Neiva Damaceno

1 reference

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26 March 2020

Norberto Ludwig-Neto

1 reference

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26 March 2020

Paulo José Cauduro Maróstica

1 reference

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26 March 2020

Samia Zahi Rached

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26 March 2020

Suzana Fonseca de Oliveira Melo

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26 March 2020

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26 March 2020

publication date

1 May 2017

1 reference

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Jornal brasileiro de pneumologia : publicaça̋o oficial da Sociedade Brasileira de Pneumologia e Tisilogia

26 March 2020

published in

1 reference

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26 March 2020

volume

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26 March 2020

issue

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26 March 2020

page(s)

219-245

1 reference

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Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation

26 March 2020

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25 May 2018

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25 May 2018

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Inhaled therapy in cystic fibrosis: agents, devices and regimens

25 May 2018

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Estimating body composition from skinfold thicknesses and bioelectrical impedance analysis in cystic fibrosis patients.

25 May 2018

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Intravenous antibiotics for pulmonary exacerbations in people with cystic fibrosis

25 May 2018

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25 May 2018

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Topical nasal steroids for treating nasal polyposis in people with cystic fibrosis

25 May 2018

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Positive expiratory pressure physiotherapy for airway clearance in people with cystic fibrosis

25 May 2018

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25 May 2018

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25 May 2018

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Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.

25 May 2018

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Microbiological diagnostic procedures for respiratory cystic fibrosis samples in Spain: towards standard of care practices.

25 May 2018

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Vitamin K supplementation for cystic fibrosis

25 May 2018

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25 May 2018

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Eradication of respiratory tract MRSA at a large adult cystic fibrosis centre

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A systematic review of factors associated with health-related quality of life in adolescents and adults with cystic fibrosis

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25 May 2018

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25 May 2018

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25 May 2018

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Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis

25 May 2018

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Oral calorie supplements for cystic fibrosis

25 May 2018

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25 May 2018

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25 May 2018

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Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation

25 May 2018

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25 May 2018

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CFTR Modulators for the Treatment of Cystic Fibrosis

25 May 2018

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Pulmonary disease in cystic fibrosis: assessment with chest CT at chest radiography dose levels

25 May 2018

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Infection prevention and control guideline for cystic fibrosis: 2013 update

25 May 2018

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25 May 2018

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Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis

25 May 2018

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Time between collection and storage significantly influences bacterial sequence composition in sputum samples from cystic fibrosis respiratory infections

25 May 2018

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CFTR functional measurements in human models for diagnosis, prognosis and personalized therapy: Report on the pre-conference meeting to the 11th ECFS Basic Science Conference, Malta, 26-29 March 2014

25 May 2018

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European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre

25 May 2018

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European Cystic Fibrosis Society Standards of Care: Best Practice guidelines

25 May 2018

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Infections in patients with cystic fibrosis: diagnostic microbiology update

25 May 2018

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Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial

25 May 2018

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Effect that an educational program for cystic fibrosis patients and caregivers has on the contamination of home nebulizers

25 May 2018

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Role of nebulized amphotericin B in the management of allergic bronchopulmonary aspergillosis in cystic fibrosis: Case report and review of literature.

25 May 2018

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Vitamin A supplementation for cystic fibrosis

25 May 2018

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Practical guidelines: lung transplantation in patients with cystic fibrosis

25 May 2018

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Bisphosphonates for osteoporosis in people with cystic fibrosis

25 May 2018

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Sweat conductivity: an accurate diagnostic test for cystic fibrosis?

25 May 2018

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Azithromycin may antagonize inhaled tobramycin when targeting Pseudomonas aeruginosa in cystic fibrosis

25 May 2018

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A new era in the treatment of cystic fibrosis: correction of the underlying CFTR defect.

25 May 2018

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Improving transition from paediatric to adult cystic fibrosis care: programme implementation and evaluation.

25 May 2018

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Australian standards of care for cystic fibrosis-related diabetes

25 May 2018

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Is chest CT useful in newborn screened infants with cystic fibrosis at 1 year of age?

25 May 2018

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Cystic fibrosis chronic rhinosinusitis: a comprehensive review

25 May 2018

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Culture-based diagnostic microbiology in cystic fibrosis: can we simplify the complexity?

25 May 2018

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Pseudomonas aeruginosa infection in patients with cystic fibrosis: scientific evidence regarding clinical impact, diagnosis, and treatment

25 May 2018

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Allergic bronchopulmonary aspergillosis: review of literature and proposal of new diagnostic and classification criteria

25 May 2018

1 reference

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Oxygen therapy for cystic fibrosis

25 May 2018

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Oral steroids for long-term use in cystic fibrosis

25 May 2018

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Oral non-steroidal anti-inflammatory drug therapy for lung disease in cystic fibrosis

25 May 2018

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Nebuliser systems for drug delivery in cystic fibrosis

25 May 2018

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Non-invasive ventilation for cystic fibrosis

25 May 2018

1 reference

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An official American Thoracic Society workshop report: optimal lung function tests for monitoring cystic fibrosis, bronchopulmonary dysplasia, and recurrent wheezing in children less than 6 years of age.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic fibrosis pulmonary guidelines. Chronic medications for maintenance of lung health

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Exogenous insulin requirements do not differ between youth and adults with cystic fibrosis related diabetes

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Assessing the Disease-Liability of Mutations in CFTR

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Macrolide antibiotics for cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Can early Burkholderia cepacia complex infection in cystic fibrosis be eradicated with antibiotic therapy?

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

State of progress in treating cystic fibrosis respiratory disease

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

CFTR biomarkers: time for promotion to surrogate end-point.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Management of allergic bronchopulmonary aspergillosis: a review and update

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

A review of pathophysiology and management of fetuses and neonates with meconium ileus for the pediatric surgeon

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Evaluation of the Bruker Biotyper and Vitek MS matrix-assisted laser desorption ionization-time of flight mass spectrometry systems for identification of nonfermenting gram-negative bacilli isolated from cultures from cystic fibrosis patients

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Prevalence of hyponatremia at diagnosis and factors associated with the longitudinal variation in serum sodium levels in infants with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

The role of exercise in maintaining health in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Chest computed tomography scores of severity are associated with future lung disease progression in children with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

End of life care for patients with cystic fibrosis.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Clinical use of dornase alpha is associated with a slower rate of FEV1 decline in cystic fibrosis.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Inhaled antibiotics for long-term therapy in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

What the pulmonary specialist should know about the new inhalation therapies

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Classification and identification of the Burkholderia cepacia complex: Past, present and future

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Duration of intravenous antibiotic therapy in people with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trial

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Assessing time to pulmonary function benefit following antibiotic treatment of acute cystic fibrosis exacerbations

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic Fibrosis Pulmonary Guidelines

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

An 18‐month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Location and duration of treatment of cystic fibrosis respiratory exacerbations do not affect outcomes

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Dornase alfa for cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Motivational interviewing for adherence problems in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic fibrosis HRCT scores correlate strongly with Pseudomonas infection

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Update on cystic fibrosis-related bone disease: a special focus on children

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Airway-clearance therapy guidelines and implementation

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effects of prolonged use of azithromycin in patients with cystic fibrosis: a meta-analysis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

The cystic fibrosis transmembrane conductance regulator in reproductive health and disease.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

High treatment burden in adults with cystic fibrosis: challenges to disease self-management

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Update on fat-soluble vitamins in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Nasal and sinus disease in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Best practice guidelines for molecular genetic diagnosis of cystic fibrosis and CFTR-related disorders--updated European recommendations

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Evidence-based practice recommendations for nutrition-related management of children and adults with cystic fibrosis and pancreatic insufficiency: results of a systematic review

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Contraceptive practices in women with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Development of a WHO growth reference for school-aged children and adolescents

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Guidelines for the management of pregnancy in women with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Clinical use of Ibuprofen is associated with slower FEV1 decline in children with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Dornase alfa is well tolerated: data from the epidemiologic registry of cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Chest radiographs for outcome assessment in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Inflammation and anti-inflammatory therapies for cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

An official ATS/IDSA statement: diagnosis, treatment, and prevention of nontuberculous mycobacterial diseases

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Long term effects of azithromycin in patients with cystic fibrosis: A double blind, placebo controlled trial

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Cystic fibrosis: terminology and diagnostic algorithms

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Dornase alfa as postoperative therapy in cystic fibrosis sinonasal disease

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Progression of lung disease on computed tomography and pulmonary function tests in children and adults with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Standards of care for patients with cystic fibrosis: a European consensus

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Guide to bone health and disease in cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Strength vs aerobic training in children with cystic fibrosis: a randomized controlled trial.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Nutrition in patients with cystic fibrosis: a European Consensus

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Prevalence and correlates of successful transfer from pediatric to adult health care among a cohort of young adults with complex congenital heart defects

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Nonclassic cystic fibrosis and CFTR-related diseases

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Non-invasive ventilation assists chest physiotherapy in adults with acute exacerbations of cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Allergic bronchopulmonary aspergillosis in cystic fibrosis--state of the art: Cystic Fibrosis Foundation Consensus Conference

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Consensus report on nutrition for pediatric patients with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effects of hypertonic saline, alternate day and daily rhDNase on healthcare use, costs and outcomes in children with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Randomized controlled study of in-hospital exercise training programs in children with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Antibiotic therapy against Pseudomonas aeruginosa in cystic fibrosis: a European consensus.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Nebulised hypertonic saline for cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Clinical outcome in relation to care in centres specialising in cystic fibrosis: cross sectional study

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Glucose tolerance in patients with cystic fibrosis: five year prospective study

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effect of high-dose ibuprofen in patients with cystic fibrosis

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Antibiotic pharmacokinetics in cystic fibrosis. Differences and clinical significance

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Liver and biliary problems in cystic fibrosis.

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Effect of ivacaftor in patients with advanced cystic fibrosis and a G551D-CFTR mutation: Safety and efficacy in an expanded access program in the United States

25 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Exercise programme in patients with cystic fibrosis: a randomized controlled trial.

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Pulmonary medication adherence and health-care use in cystic fibrosis

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Distal intestinal obstruction syndrome in cystic fibrosis: presentation, outcome and management in a tertiary hospital (2007-2012).

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

HRCT and MRI of the lung in children with cystic fibrosis: comparison of different scoring systems.

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Eradication of chronic methicillin-resistant Staphylococcus aureus infection in cystic fibrosis patients. An observational prospective cohort study of 11 patients.

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

The strategic role of the nurse in the selection of IV devices

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Omalizumab in the management of steroid dependent allergic bronchopulmonary aspergillosis (ABPA) complicating cystic fibrosis

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Baby bottle steam sterilizers disinfect home nebulizers inoculated with bacterial respiratory pathogens

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Evolution of pancreatic function during the first year in infants with cystic fibrosis

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Evaluation of a cystic fibrosis transition program from pediatric to adult care

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Comparison of two treatment regimens for eradication of Pseudomonas aeruginosa infection in children with cystic fibrosis

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

A network meta-analysis of the efficacy of inhaled antibiotics for chronic Pseudomonas infections in cystic fibrosis

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Oral contraceptives do not appear to affect cystic fibrosis disease severity

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Long-term inhaled dry powder mannitol in cystic fibrosis: an international randomized study.

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Sinonasal inhalation of dornase alfa in CF: A double-blind placebo-controlled cross-over pilot trial

15 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5687954

Dornase alfa improves the health-related quality of life among Brazilian patients with cystic fibrosis--a one-year prospective study

15 August 2018

1 reference

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Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis

15 August 2018

1 reference

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15 August 2018

1 reference

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15 August 2018

1 reference

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15 August 2018

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15 August 2018

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15 August 2018

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15 August 2018

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Incidence of cystic fibrosis in five different states of Brazil as determined by screening of p.F508del, mutation at the CFTR gene in newborns and patients

15 August 2018

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15 August 2018

1 reference

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15 August 2018

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DNase in stable cystic fibrosis infants: a pilot study

15 August 2018

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15 August 2018

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Sweat conductivity and chloride titration for cystic fibrosis diagnosis in 3834 subjects

15 August 2018

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15 August 2018

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A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities

15 August 2018

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15 August 2018

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A comparison of the efficacy and tolerance of pancrelipase and placebo in the treatment of steatorrhea in cystic fibrosis patients with clinical exocrine pancreatic insufficiency

15 August 2018

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15 August 2018

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12 December 2020

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12 December 2020

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12 December 2020

Cholecalciferol significantly increases 25-hydroxyvitamin D concentrations in adults with cystic fibrosis

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12 December 2020

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12 December 2020

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12 December 2020

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12 December 2020

Segregation is good for patients with cystic fibrosis

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12 December 2020

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12 December 2020

Pooled analysis of two large randomised phase III inhaled mannitol studies in cystic fibrosis

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12 December 2020

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12 December 2020

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12 December 2020

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12 December 2020

Use of ibuprofen to assess inflammatory biomarkers in induced sputum: Implications for clinical trials in cystic fibrosis

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12 December 2020

Treatment burden and health-related quality of life of children with diabetes, cystic fibrosis and asthma

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12 December 2020

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12 December 2020

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Point: does the risk of cross infection warrant exclusion of adults with cystic fibrosis from cystic fibrosis foundation events? Yes

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12 December 2020

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12 December 2020

Long-term multicentre randomised controlled study of high frequency chest wall oscillation versus positive expiratory pressure mask in cystic fibrosis

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Randomised double blind placebo controlled trial investigating the effect of calcium and vitamin D supplementation on bone mineral density and bone metabolism in adult patients with cystic fibrosis

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12 December 2020

Safety and cleaning of medical materials and devices

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12 December 2020

[Neonatal cystic fibrosis screening program in the state of Paraná: evaluation 30 months after implementation]

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12 December 2020

How long should we maintain long-term azithromycin treatment in cystic fibrosis patients?

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12 December 2020

Successful decolonization of methicillin-resistant Staphylococcus aureus in paediatric patients with cystic fibrosis (CF) using a three-step protocol

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12 December 2020

A prospective treatment trial of nasal polyps in adults with cystic fibrosis

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12 December 2020

Bronchiectasis: comparison of preoperative thin-section CT and pathologic findings in resected specimens

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10.1590/S1806-37562017000000065

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28746534%20AND%20SRC:MED&resulttype=core&format=json

26 March 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28746534%20AND%20SRC:MED&resulttype=core&format=json

26 March 2020

PubMed publication ID

28746534

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28746534%20AND%20SRC:MED&resulttype=core&format=json