Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1. (Q47991885)

7 February 2018

title

Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1. (English)

1 reference

7 February 2018

0 references

1 reference

7 February 2018

Huda Zoghbi

1 reference

7 February 2018

author name string

Cummings CJ

1 reference

7 February 2018

Mancini MA

1 reference

7 February 2018

Antalffy B

1 reference

7 February 2018

DeFranco DB

1 reference

7 February 2018

language of work or name

English

0 references

publication date

1 June 1998

1 reference

7 February 2018

published in

Nature Genetics

1 reference

7 February 2018

volume

1 reference

7 February 2018

issue

1 reference

7 February 2018

page(s)

148-154

1 reference

7 February 2018

Biology of A beta amyloid in Alzheimer's disease

cites work

1 reference

Mutation in the alpha-synuclein gene identified in families with Parkinson's disease

21 January 2018

1 reference

Prion Diseases and the BSE Crisis

21 January 2018

1 reference

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

21 January 2018

1 reference

Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

21 January 2018

1 reference

Suppression of aggregate formation and apoptosis by transglutaminase inhibitors in cells expressing truncated DRPLA protein with an expanded polyglutamine stretch.

21 January 2018

1 reference

Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

21 January 2018

1 reference

Intranuclear inclusions of expanded polyglutamine protein in spinocerebellar ataxia type 3.

21 January 2018

1 reference

Spinocerebellar ataxia type 1

21 January 2018

1 reference

Glutamine repeats as polar zippers: their possible role in inherited neurodegenerative diseases

21 January 2018

1 reference

Incorporation of glutamine repeats makes protein oligomerize: implications for neurodegenerative diseases

21 January 2018

1 reference

The ubiquitin system for protein degradation

21 January 2018

1 reference

Ubiquitin-dependent protein degradation

21 January 2018

1 reference

Structure and functions of the 20S and 26S proteasomes

21 January 2018

1 reference

Proteasome inhibition leads to a heat-shock response, induction of endoplasmic reticulum chaperones, and thermotolerance

21 January 2018

1 reference

Proteasome inhibitors cause induction of heat shock proteins and trehalose, which together confer thermotolerance in Saccharomyces cerevisiae

21 January 2018

1 reference

The Hsp70 and Hsp60 chaperone machines

21 January 2018

1 reference

Molecular chaperones in cellular protein folding

21 January 2018

1 reference

Molecular chaperone functions of heat-shock proteins

21 January 2018

1 reference

Escherichia coli heat shock gene mutants are defective in proteolysis

21 January 2018

1 reference

Involvement of the molecular chaperone Ydj1 in the ubiquitin-dependent degradation of short-lived and abnormal proteins in Saccharomyces cerevisiae

21 January 2018

1 reference

SCA1 transgenic mice: A model for neurodegeneration caused by an expanded CAG trinucleotide repeat

21 January 2018

1 reference

Expression of subunits of the 19S complex and of the PA28 activator in rat skeletal muscle.

21 January 2018

1 reference

Cloning of a unique human homologue of the Escherichia coli DNAJ heat shock protein

21 January 2018

1 reference

Human cDNA encoding DnaJ protein homologue

21 January 2018

1 reference

A role for HDJ-2/HSDJ in correcting subnuclear trafficking, transactivation, and transrepression defects of a glucocorticoid receptor zinc finger mutant

21 January 2018

1 reference

Interactions of the chaperone Hsp104 with yeast Sup35 and mammalian PrP.

21 January 2018

1 reference

Chaperone-supervised conversion of prion protein to its protease-resistant form

21 January 2018

1 reference

Chaperoning brain diseases

21 January 2018

1 reference

Role of the chaperone protein Hsp104 in propagation of the yeast prion-like factor [psi+]

21 January 2018

1 reference

DnaJ-like proteins: molecular chaperones and specific regulators of Hsp70.

21 January 2018

1 reference

Synthesis of heat shock proteins in rat brain cortex after transient ischemia

21 January 2018

1 reference

Induction of heat shock (stress) genes in the mammalian brain by hyperthermia and other traumatic events: a current perspective

21 January 2018

1 reference

Cooperation of the molecular chaperone Ydj1 with specific Hsp70 homologs to suppress protein aggregation

21 January 2018

1 reference

The cerebellar leucine-rich acidic nuclear protein interacts with ataxin-1

21 January 2018

1 reference

Expression analysis of the ataxin-1 protein in tissues from normal and spinocerebellar ataxia type 1 individuals

21 January 2018

1 reference

Structural and functional effects of PA700 and modulator protein on proteasomes 1 1Edited by W. Baumeister

21 January 2018

1 reference

7 January 2021

The conserved carboxyl terminus and zinc finger-like domain of the co-chaperone Ydj1 assist Hsp70 in protein folding

1 reference

7 January 2021

Cooperative action of Hsp70, Hsp90, and DnaJ proteins in protein renaturation

1 reference

7 January 2021

Sodium Dodecyl Sulfate (SDS) Activation of the 20S Proteasome in Rat Liver

1 reference

7 January 2021

Identifiers

DOI

10.1038/502

1 reference

7 February 2018

1 reference

7 February 2018