The human GM2 activator protein. A substrate specific cofactor of beta-hexosaminidase A (Q45781361)

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18 September 2019

title

The human GM2 activator protein. A substrate specific cofactor of beta-hexosaminidase A (English)

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18 September 2019

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3 December 2022

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3 December 2022

E. M. Meier

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3 December 2022

G. Schwarzmann

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3 December 2022

W. Fürst

series ordinal

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3 December 2022

K. Sandhoff

series ordinal

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3 December 2022

language of work or name

English

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publication date

1 January 1991

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18 September 2019

25 January 1991

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National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=1824846

full work available at URL

3 December 2022

http://intl.jbc.org/cgi/content/abstract/266/3/1879

online access status

open access

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https://api.elsevier.com/content/article/PII:S0021925818523759?httpAccept=text/xml

3 December 2022

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DOI

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

https://api.elsevier.com/content/article/PII:S0021925818523759?httpAccept=text/plain

3 December 2022

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DOI

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Journal of Biological Chemistry

3 December 2022

published in

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18 September 2019

volume

266

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18 September 2019

issue

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18 September 2019

page(s)

1879-1887

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Characterization of the phospholipid requirement of a rat liver beta-glucosidase

18 September 2019

cites work

1 reference

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A difference in the specificities of human liver N-acetyl-beta-hexosaminidases A and B detected by their activities towards glycosaminoglycan oligosaccharides

3 December 2022

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Subunit structure of human hexosaminidase verified: interconvertibility of hexosaminidase isozymes

3 December 2022

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A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

3 December 2022

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Activating Proteins for Ganglioside GM2Degradation by β-Hexosaminidase Isoenzymes in Tissue Extracts from Different Species

3 December 2022

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Isolation of two forms of an activator protein for the enzymic sphingomyelin degradation from human Gaucher spleen

3 December 2022

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AB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2

3 December 2022

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Purification and Characterization of an Activator Protein for the Degradation of Glycolipids GM2and GA2by Hexosaminidase A

3 December 2022

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Complexing of Glycolipids and Their Transfer between Membranes by the Activator Protein for Degradation of Lysosomal Ganglioside GM2

3 December 2022

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Analysis of gangliosides using fast atom bombardment mass spectrometry

3 December 2022

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The Activator of Cerebroside Sulphatase. Purification from Human Liver and Identification as a Protein

3 December 2022

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The activator of cerebroside-sulphatase. A model of the activation

3 December 2022

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A simple method for the isolation and purification of total lipides from animal tissues

3 December 2022

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The structure of lipid bilayers and the effects of general anaesthetics. An x-ray and neutron diffraction study.

3 December 2022

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Impaired degradation of keratan sulphate by Morquio A fibroblasts

3 December 2022

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Gaucher's disease: deficiency of 'acid' -glucosidase and reconstitution of enzyme activity in vitro

3 December 2022

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Immunological evidence for deficiency in an activator protein for sulfatide sulfatase in a variant form of metachromatic leukodystrophy

3 December 2022

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Ganglioside-composition of brain in Tay-Sachs disease: increased amounts of GD2 and N-acetyl-beta-D-galactosaminyl GD1a ganglioside

3 December 2022

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The cohydrolases in human spleen that stimulate glucosyl ceramide beta-glucosidase

3 December 2022

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Multilayers of Phospholipid Bimolecular Leaflets

3 December 2022

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A new variant of Type-AB GM2-gangliosidosis

3 December 2022

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Protein measurement with the Folin phenol reagent

3 December 2022

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Structure of full-length cDNA coding for sulfatide activator, a Co-beta-glucosidase and two other homologous proteins: two alternate forms of the sulfatide activator

3 December 2022

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Mutation in GM2-gangliosidosis B1 variant

3 December 2022

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Tay-Sachs Disease: Generalized Absence of a Beta-D- N -Acetylhexosaminidase Component

3 December 2022

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An evaluation of film detection methods for weak beta-emitters, particularly tritium

3 December 2022

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Composition of gangliosides and neutral glycosphingolipids of brain in classical Tay-Sachs and Sandhoff disease: more lyso-GM2 in Sandhoff disease?

3 December 2022

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Variation of beta-N-acetylhexosaminidase-pattern in Tay-Sachs disease

3 December 2022

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Enzyme alterations and lipid storage in three variants of Tay-Sachs disease

3 December 2022

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Specificity of human liver hexosaminidases A and B against glycosphingolipids GM2 and GA2. Purification of the enzymes by affinity chromatography employing specific elution

3 December 2022

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A simple and novel method for tritium labeling of gangliosides and other sphingolipids

3 December 2022

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Lysogangliosides: synthesis and use in preparing labeled gangliosides

3 December 2022

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Incorporation of ganglioside analogs into fibroblast cell membranes. A spin-label study

3 December 2022

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Incorporation and metabolism of ganglioside GM2 in skin fibroblasts from normal and GM2 gangliosidosis subjects.

3 December 2022

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Genetic complementation in somatic cell hybrids of four variants of infantile GM2 gangliosidosis

3 December 2022

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Quantitative estimation of sialic acids. II. A colorimetric resorcinol-hydrochloric acid method

3 December 2022

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GM2-gangliosidosis B1 variant: a wide geographic and ethnic distribution of the specific beta-hexosaminidase alpha chain mutation originally identified in a Puerto Rican patient

3 December 2022

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N-acetyl-beta-hexosaminidase: role in the degradation of glycosaminoglycans

3 December 2022

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Release of Sphingomyelin Phosphodiesterase (Acid Sphingomyelinase) by Ammonium Chloride from CL 1D Mouse L-Cells and Human Fibroblasts. Partial Purification and Characterization of the Exported Enzymes

3 December 2022

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Calculation of the conformation of glycosphingolipids. 2. GM1- and GM2-gangliosides

3 December 2022

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Calculation of the conformation of glycosphingolipids. 1. Beta-D-glucosyl-N-(2-D-hydroxyoctadecanoyl)-D-dihydrosphingosine (glucosyl-ceramide) and alpha-D-N-acetylneuraminyl-(2----3)-beta-D-galactose

3 December 2022

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Characterization of some minor gangliosides in Tay-Sachs brains

3 December 2022

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Neutron diffraction studies on phosphatidylcholine model membranes. II. Chain conformation and segmental disorder

3 December 2022

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3 December 2022

Identifiers

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