Upshaw-Schulman syndrome revisited: a concept of congenital thrombotic thrombocytopenic purpura (Q33338776)

25 July 2017

title

Upshaw-Schulman syndrome revisited: a concept of congenital thrombotic thrombocytopenic purpura (English)

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thrombotic thrombocytopenic purpura

25 July 2017

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S Kinoshita

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25 July 2017

A Yoshioka

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25 July 2017

Y D Park

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25 July 2017

H Ishizashi

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25 July 2017

M Konno

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25 July 2017

M Funato

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25 July 2017

T Matsui

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25 July 2017

K Titani

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25 July 2017

H Yagi

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25 July 2017

M Matsumoto

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25 July 2017

Y Fujimura

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25 July 2017

publication date

1 July 2001

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International Journal of Hematology

25 July 2017

published in

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25 July 2017

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25 July 2017

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25 July 2017

page(s)

101-108

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Fibronectin levels in congenital thrombocytopenia: Schulman's syndrome

25 July 2017

cites work

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12 December 2020

Shear-dependent changes in the three-dimensional structure of human von Willebrand factor

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12 December 2020

Thrombopoietin in Upshaw-Schulman syndrome

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12 December 2020

Luminographic detection of von Willebrand factor multimers in agarose gels and on nitrocellulose membranes

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12 December 2020

Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura.

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12 December 2020

von Willebrand factor

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12 December 2020

Involvement of large plasma von Willebrand factor (vWF) multimers and unusually large vWF forms derived from endothelial cells in shear stress-induced platelet aggregation

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12 December 2020

Chronic relapsing thrombocytopenic purpura with severe neurological manifestations and full recovery.

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12 December 2020

Studies on thrombopoiesis. I. A factor in normal human plasma required for platelet production; chronic thrombocytopenia due to its deficiency

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12 December 2020

Letter: A more uniform measurement of factor VIII inhibitors

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12 December 2020

ABO blood group genotype and plasma von Willebrand factor in normal individuals.

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12 December 2020

Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura

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12 December 2020

Total inhibition of high shear stress induced platelet aggregation by homodimeric von Willebrand factor A1-loop fragments

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12 December 2020

Partial clinical improvement in Upshaw-Schulman syndrome following prostacyclin infusion.

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12 December 2020

Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion.

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12 December 2020

Upshaw-Schulman Syndrome and Fibronectin (Cold-Insoluble Globulin)

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12 December 2020

Recovery and half-life of von Willebrand factor-cleaving protease after plasma therapy in patients with thrombotic thrombocytopenic purpura

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12 December 2020

Factor VIII concentrate-responsive thrombocytopenia, hemolytic anemia, and nephropathy. Evidence that factor VIII:von Willebrand factor is involved in its pathogenesis

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12 December 2020

Efficacy of several plasma components in a young boy with chronic thrombocytopenia and hemolytic anemia who responds repeatedly to normal plasma infusions

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12 December 2020

von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome

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12 December 2020

Decreased cold-insoluble globulin in congenital thrombocytopenia (Upshaw-Schulman syndrome)

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12 December 2020

Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura

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12 December 2020

Variant von Willebrand's disease: characterization of two subtypes by analysis of multimeric composition of factor VIII/von Willebrand factor in plasma and platelets

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12 December 2020

Congenital deficiency of a factor in normal plasma that reverses microangiopathic hemolysis and thrombocytopenia

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12 December 2020

Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis.

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12 December 2020

von Willebrand factor. A reduced and alkylated 52/48-kDa fragment beginning at amino acid residue 449 contains the domain interacting with platelet glycoprotein Ib.

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12 December 2020

Identifiers

DOI

10.1007/BF02982558

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Dimensions Publication ID

25 July 2017

1012526850

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