Direct block of the cystic fibrosis transmembrane conductance regulator Cl(-) channel by butyrate and phenylbutyrate (Q31869423)

4 July 2017

title

Direct block of the cystic fibrosis transmembrane conductance regulator Cl(-) channel by butyrate and phenylbutyrate (English)

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4 July 2017

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transmembrane protein

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author name string

Linsdell P

series ordinal

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4 July 2017

language of work or name

English

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publication date

1 January 2001

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European Journal of Pharmacology

4 July 2017

published in

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4 July 2017

volume

411

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4 July 2017

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4 July 2017

page(s)

255-260

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Activation of deltaF508 CFTR in a cystic fibrosis respiratory epithelial cell line by 4-phenylbutyrate, genistein and CPX.

4 July 2017

cites work

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Chemical chaperones correct the mutant phenotype of the ΔF508 cystic fibrosis transmembrane conductance regulator protein

7 January 2021

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Removal of multiple arginine-framed trafficking signals overcomes misprocessing of delta F508 CFTR present in most patients with cystic fibrosis

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Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

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Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

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Disulphonic stilbene block of cystic fibrosis transmembrane conductance regulator Cl- channels expressed in a mammalian cell line and its regulation by a critical pore residue

7 January 2021

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Flickery block of single CFTR chloride channels by intracellular anions and osmolytes

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Adenosine triphosphate-dependent asymmetry of anion permeation in the cystic fibrosis transmembrane conductance regulator chloride channel

7 January 2021

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Substrates of multidrug resistance-associated proteins block the cystic fibrosis transmembrane conductance regulator chloride channel

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Multi-Ion Mechanism for Ion Permeation and Block in the Cystic Fibrosis Transmembrane Conductance Regulator Chloride Channel

7 January 2021

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Non-pore lining amino acid side chains influence anion selectivity of the human CFTR Cl- channel expressed in mammalian cell lines

7 January 2021

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Molecular determinants of anion selectivity in the cystic fibrosis transmembrane conductance regulator chloride channel pore

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Mechanism of Glibenclamide Inhibition of Cystic Fibrosis Transmembrane Conductance Regulator Cl− Channels Expressed in a Murine Cell Line

7 January 2021

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7 January 2021

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Ionic Blockage of Sodium Channels in Nerve

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10.1016/S0014-2999(00)00928-6

7 January 2021

Identifiers

DOI

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4 July 2017

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