Defects in Neuromuscular Transmission May Underlie Motor Dysfunction in Spinal and Bulbar Muscular Atrophy (Q36863987)

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3 April 2020

title

Defects in Neuromuscular Transmission May Underlie Motor Dysfunction in Spinal and Bulbar Muscular Atrophy (English)

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Cynthia L Jordan

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3 April 2020

Katherine Halievski

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Masahisa Katsuno

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Youfen Xu

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William D Atchison

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Gen Sobue

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language of work or name

English

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publication date

1 May 2016

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published in

Journal of Neuroscience

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volume

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issue

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3 April 2020

page(s)

5094-5106

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Androgen-dependent loss of muscle BDNF mRNA in two mouse models of SBMA.

3 April 2020

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Androgen receptor YAC transgenic mice recapitulate SBMA motor neuronopathy and implicate VEGF164 in the motor neuron degeneration

29 September 2017

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29 September 2017

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29 September 2017

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27 June 2018

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27 June 2018

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27 June 2018

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27 June 2018

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27 June 2018

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Increased neurotransmitter release at the neuromuscular junction in a mouse model of polyglutamine disease

4 September 2018

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4 September 2018

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4 September 2018

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Acetylcholine receptor gamma-subunits mRNA isoforms expressed in denervated rat muscle

4 September 2018

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Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration.

4 September 2018

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BDNF increases release probability and the size of a rapidly recycling vesicle pool within rat hippocampal excitatory synapses

4 September 2018

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4 September 2018

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Regulation of transmitter release by synapsin II in mouse motor terminals

4 September 2018

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4 September 2018

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Testosterone reduction prevents phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy

4 September 2018

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Brain-derived neurotrophic factor modulates cerebellar plasticity and synaptic ultrastructure.

4 September 2018

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Increased sodium conductance in the synaptic region of rat skeletal muscle fibres.

4 September 2018

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Lack of synapsin I reduces the readily releasable pool of synaptic vesicles at central inhibitory synapses

4 September 2018

1 reference

12 December 2020

Synapsins as mediators of BDNF-enhanced neurotransmitter release

1 reference

12 December 2020

Inhibiting axon degeneration and synapse loss attenuates apoptosis and disease progression in a mouse model of motoneuron disease

1 reference

12 December 2020

Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man

1 reference

12 December 2020

A quantitative study of end-plate potentials in isolated human muscle

1 reference

12 December 2020

A comparative electrophysiological study of motor end-plate diseased skeletal muscle in the mouse

1 reference

12 December 2020

X-linked recessive bulbospinal neuronopathy. A clinicopathological study

1 reference

12 December 2020

Androgen receptor expression in the levator ani muscle of male mice

1 reference

12 December 2020

Active Zones and the Readily Releasable Pool of Synaptic Vesicles at the Neuromuscular Junction of the Mouse

1 reference

12 December 2020

10.1523/JNEUROSCI.3485-15.2016

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27147661%20AND%20SRC:MED&resulttype=core&format=json

3 April 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27147661%20AND%20SRC:MED&resulttype=core&format=json

3 April 2020

PubMed publication ID

27147661

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27147661%20AND%20SRC:MED&resulttype=core&format=json