The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies. (Q35859776)

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31 December 2019

review article

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title

The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies (English)

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15303000%20AND%20SRC:MED&resulttype=core&format=json

31 December 2019

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31 December 2019

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31 December 2019

M Wajner

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31 December 2019

C S Dutra-Filho

series ordinal

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31 December 2019

publication date

1 January 2004

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Journal of Inherited Metabolic Disease

31 December 2019

published in

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31 December 2019

volume

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31 December 2019

issue

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31 December 2019

page(s)

427-448

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CT and MR of the brain in the diagnosis of organic acidemias. Experiences from 107 patients

31 December 2019

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Induction of oxidative stress in rat brain by the metabolites accumulating in maple syrup urine disease.

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Intrastriatal administration of 3-hydroxyglutaric acid induces convulsions and striatal lesions in rats

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Induction of oxidative stress by L-2-hydroxyglutaric acid in rat brain

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Ascorbic acid and alpha-tocopherol attenuate methylmalonic acid-induced convulsions

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Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease

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Inhibition of mitochondrial creatine kinase activity by D-2-hydroxyglutaric acid in cerebellum of young rats.

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Crossref

https://api.crossref.org/works/10.1023%2FB%3ABOLI.0000037353.13085.E2

7 January 2021