Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response (Q34103354)

31 July 2017

title

Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response (English)

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31 July 2017

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Tatiana V Cohen

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31 July 2017

Jonathan E Cohen

series ordinal

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31 July 2017

Terence A Partridge

series ordinal

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31 July 2017

publication date

3 May 2012

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31 July 2017

published in

Neuromuscular Disorders

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31 July 2017

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31 July 2017

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31 July 2017

page(s)

648-658

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describes a project that uses

31 July 2017

ImageJ

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC4147957/fullTextXML

inferred from PubMed Central ID database lookup

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Dysferlin is a plasma membrane protein and is expressed early in human development

5 July 2018

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Dysferlin, a novel skeletal muscle gene, is mutated in Miyoshi myopathy and limb girdle muscular dystrophy

5 July 2018

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5 July 2018

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5 July 2018

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A gene for autosomal recessive limb-girdle muscular dystrophy maps to chromosome 2p

5 July 2018

1 reference

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Muscle membrane repair and inflammatory attack in dysferlinopathy.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Role of thrombospondin 1 in macrophage inflammation in dysferlin myopathy.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Absence of dysferlin alters myogenin expression and delays human muscle differentiation "in vitro".

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Disruption of muscle membrane and phenotype divergence in two novel mouse models of dysferlin deficiency

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlinopathy (LGMD2B): a 23-year follow-up study of 10 patients homozygous for the same frameshifting dysferlin mutations.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlin deletion in SJL mice (SJL-Dysf) defines a natural model for limb girdle muscular dystrophy 2B

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Intrinsic differences in MyoD and myogenin expression between primary cultures of SJL/J and BALB/C skeletal muscle

28 October 2018

1 reference

12 December 2020

Spontaneous myopathy in the SJL/J mouse: pathology and strength loss

1 reference

12 December 2020

Histological assessment of SJL/J mice treated with the antioxidants coenzyme Q10 and resveratrol

1 reference

12 December 2020

The genotype of bone marrow-derived inflammatory cells does not account for differences in skeletal muscle regeneration between SJL/J and BALB/c mice

1 reference

12 December 2020

Muscle pathology in dysferlin deficiency

1 reference

12 December 2020

10.1016/J.NMD.2012.03.002

Identifiers

DOI

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31 July 2017

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31 July 2017

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