Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences (Q26747210)

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15 March 2020

review article

4 references

28 January 2021

6 February 2021

27 January 2024

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences (English)

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15 March 2020

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28 January 2021

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15 December 2019

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6 February 2021

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15 March 2020

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15 March 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

1 reference

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15 March 2020

Noel G McElvaney

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15 March 2020

language of work or name

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publication date

1 June 2016

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15 December 2019

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15 March 2020

28 January 2021

6 February 2021

27 January 2024

BioMed Research International

10 references

13 March 2019

21 March 2019

22 April 2019

28 November 2019

15 December 2019

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

28 January 2021

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27 January 2024

2016

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15 March 2020

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Creative Commons Attribution 4.0 International

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28 September 2017

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28 September 2017

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Effect of increasing doses of hypertonic saline on mucociliary clearance in patients with cystic fibrosis

28 September 2017

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28 September 2017

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28 September 2017

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28 September 2017

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Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice

28 September 2017

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Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin

28 September 2017

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An animal model for cystic fibrosis made by gene targeting

28 September 2017

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Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor

28 September 2017

1 reference

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Cystic fibrosis and infertility caused by congenital bilateral absence of the vas deferens and related clinical entities

28 September 2017

1 reference

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CFTR is required for PKA-regulated ATP sensitivity of Kir1.1 potassium channels in mouse kidney

28 September 2017

1 reference

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Lysozyme secretion by submucosal glands protects the airway from bacterial infection.

31 May 2018

1 reference

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CFTR gene and male fertility

31 May 2018

1 reference

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Lower airway inflammation in infants and young children with cystic fibrosis

31 May 2018

1 reference

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Cystic fibrosis in the mouse by targeted insertional mutagenesis

31 May 2018

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Gastrointestinal Manifestations of Cystic Fibrosis.

31 May 2018

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Production of a severe cystic fibrosis mutation in mice by gene targeting

21 January 2018

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A severe phenotype in mice with a duplication of exon 3 in the cystic fibrosis locus.

21 January 2018

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Generation and characterization of a delta F508 cystic fibrosis mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

The severe G480C cystic fibrosis mutation, when replicated in the mouse, demonstrates mistrafficking, normal survival and organ-specific bioelectrics

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Long-term survival of the exon 10 insertional cystic fibrosis mutant mouse is a consequence of low level residual wild-type Cftr gene expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Zero-stress state of intra- and extraparenchymal airways from human, pig, rabbit, and sheep lung.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Morphometric characterization of the airway and vascular systems of the lung of the domestic pig, Sus scrofa: comparison of the airway, arterial and venous systems

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Evolution of pancreatic function during the first year in infants with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Successful targeting of the mouse cystic fibrosis transmembrane conductance regulator gene in embryonal stem cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

The CF mouse: an important tool for studying cystic fibrosis.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Normal vas deferens in fetuses with cystic fibrosis

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient

28 November 2018

1 reference

12 December 2020

Blood basophils from cystic fibrosis patients with allergic bronchopulmonary aspergillosis are primed and hyper-responsive to stimulation by aspergillus allergens

1 reference

12 December 2020

Colonic diverticulitis causing partial bowel obstruction in a child with cystic fibrosis

1 reference

12 December 2020

cAMP- but not Ca(2+)-regulated Cl- conductance is lacking in cystic fibrosis mice epididymides and seminal vesicles

1 reference

12 December 2020

The respiratory tract immune system in the pig. II. associated lymphoid tissues

1 reference

12 December 2020

Severe phenotype in mice with termination mutation in exon 2 of cystic fibrosis gene

1 reference

12 December 2020

The delta F508 mutation decreases the stability of cystic fibrosis transmembrane conductance regulator in the plasma membrane. Determination of functional half-lives on transfected cells

1 reference

12 December 2020

Longitudinal assessment of Pseudomonas aeruginosa in young children with cystic fibrosis

1 reference

12 December 2020

1 reference

12 December 2020

Impaired ability of Cftr knockout mice to control lung infection with Pseudomonas aeruginosa.

1 reference

12 December 2020

Early Pulmonary Inflammation in Infants with Cystic Fibrosis

1 reference

12 December 2020

Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation

1 reference

12 December 2020

Submucosal glands are the predominant site of CFTR expression in the human bronchus

1 reference

12 December 2020

True survival benefit of lung transplantation for cystic fibrosis patients: the Zurich experience

1 reference

12 December 2020

Identifiers

DOI

10.1155/2016/5258727

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

1 reference

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

PubMed publication ID

27340661

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json