(Q36556391)

14 August 2017

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title

Cystic fibrosis mouse models (English)

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14 August 2017

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Danuta Radzioch

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Gregory P Downey

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Claudine Guilbault

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14 August 2017

Zienab Saeed

series ordinal

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14 August 2017

publication date

3 August 2006

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American Journal of Respiratory Cell and Molecular Biology

14 August 2017

published in

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14 August 2017

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14 August 2017

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14 August 2017

page(s)

1-7

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An animal model for cystic fibrosis made by gene targeting

14 August 2017

cites work

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The severe G480C cystic fibrosis mutation, when replicated in the mouse, demonstrates mistrafficking, normal survival and organ-specific bioelectrics

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Talniflumate increases survival in a cystic fibrosis mouse model of distal intestinal obstructive syndrome

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A membrane lipid imbalance plays a role in the phenotypic expression of cystic fibrosis in cftr(-/-) mice

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Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice

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Murine submucosal glands are clonally derived and show a cystic fibrosis gene-dependent distribution pattern

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Innate lung defenses and compromised Pseudomonas aeruginosa clearance in the malnourished mouse model of respiratory infections in cystic fibrosis

21 January 2018

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Mapping of genetic factors influencing the weight of cystic fibrosis knockout mice

21 January 2018

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Increased Rate of Fractures and Severe Kyphosis: Sequelae of Living into Adulthood with Cystic Fibrosis

21 January 2018

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CFTR as a cAMP-dependent regulator of sodium channels

21 January 2018

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Murine models of chronic Pseudomonas aeruginosa lung infection

21 January 2018

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Excessive inflammatory response of cystic fibrosis mice to bronchopulmonary infection with Pseudomonas aeruginosa

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Nonmucoid Pseudomonas aeruginosa expresses alginate in the lungs of patients with cystic fibrosis and in a mouse model.

21 January 2018

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Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice

21 January 2018

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Response to acute lung infection with mucoid Pseudomonas aeruginosa in cystic fibrosis mice

21 January 2018

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Gene complementation of airway epithelium in the cystic fibrosis mouse is necessary and sufficient to correct the pathogen clearance and inflammatory abnormalities

21 January 2018

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Novel mouse model of chronic Pseudomonas aeruginosa lung infection mimicking cystic fibrosis

21 January 2018

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Intranasal immunization strategy to impede pilin-mediated binding of Pseudomonas aeruginosa to airway epithelial cells

21 January 2018

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Identification of DNA markers for a transmissible Pseudomonas aeruginosa cystic fibrosis strain

21 January 2018

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Enhanced susceptibility to pulmonary infection with Burkholderia cepacia in Cftr(-/-) mice

21 January 2018

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Neutrophil transepithelial migration: role of toll-like receptors in mucosal inflammation

21 January 2018

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21 January 2018

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Lung inflammation as a therapeutic target in cystic fibrosis.

21 January 2018

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Nutritional effects on host response to lung infections with mucoid Pseudomonas aeruginosa in mice

21 January 2018

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Characterization of LPS-induced lung inflammation in cftr-/- mice and the effect of docosahexaenoic acid

21 January 2018

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21 January 2018

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Modulation of deltaF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids

21 January 2018

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Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects

21 January 2018

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SERCA pump inhibitors do not correct biosynthetic arrest of deltaF508 CFTR in cystic fibrosis

21 January 2018

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Embryonic stem cells generate airway epithelial tissue

21 January 2018

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Successful targeting of the mouse cystic fibrosis transmembrane conductance regulator gene in embryonal stem cells

21 January 2018

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Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation

21 January 2018

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21 January 2018

Identifiers

DOI

10.1165/RCMB.2006-0184TR

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14 August 2017

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