(Q34103354)

31 July 2017

title

Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response (English)

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31 July 2017

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Tatiana V Cohen

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31 July 2017

Jonathan E Cohen

series ordinal

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31 July 2017

Terence A Partridge

series ordinal

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31 July 2017

publication date

3 May 2012

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31 July 2017

published in

Neuromuscular Disorders

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31 July 2017

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31 July 2017

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31 July 2017

page(s)

648-658

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describes a project that uses

31 July 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC4147957/fullTextXML

inferred from PubMed Central ID database lookup

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5 July 2018

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5 July 2018

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Dexamethasone induces dysferlin in myoblasts and enhances their myogenic differentiation

5 July 2018

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Extensive mononuclear infiltration and myogenesis characterize recovery of dysferlin-null skeletal muscle from contraction-induced injuries

5 July 2018

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Genetic manipulation of dysferlin expression in skeletal muscle: novel insights into muscular dystrophy

5 July 2018

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5 July 2018

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Attenuated muscle regeneration is a key factor in dysferlin-deficient muscular dystrophy

5 July 2018

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5 July 2018

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5 July 2018

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NF-kappaB regulation of YY1 inhibits skeletal myogenesis through transcriptional silencing of myofibrillar genes.

5 July 2018

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Interplay of IKK/NF-kappaB signaling in macrophages and myofibers promotes muscle degeneration in Duchenne muscular dystrophy

5 July 2018

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From T-tubule to sarcolemma: damage-induced dysferlin translocation in early myogenesis

5 July 2018

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Celastrol, a novel triterpene, potentiates TNF-induced apoptosis and suppresses invasion of tumor cells by inhibiting NF-kappaB-regulated gene products and TAK1-mediated NF-kappaB activation

5 July 2018

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5 July 2018

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Normal myoblast fusion requires myoferlin

5 July 2018

1 reference

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Ultrastructural changes in dysferlinopathy support defective membrane repair mechanism

5 July 2018

1 reference

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Dysferlin and the plasma membrane repair in muscular dystrophy

5 July 2018

1 reference

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5 July 2018

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Defective membrane repair in dysferlin-deficient muscular dystrophy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

IL-1beta stimulates IL-6 production in cultured skeletal muscle cells through activation of MAP kinase signaling pathway and NF-kappa B.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Plasma membrane repair is mediated by Ca(2+)-regulated exocytosis of lysosomes

5 July 2018

1 reference

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A new mathematical model for relative quantification in real-time RT-PCR

5 July 2018

1 reference

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Distal anterior compartment myopathy: a dysferlin mutation causing a new muscular dystrophy phenotype

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

NF-kappaB-induced loss of MyoD messenger RNA: possible role in muscle decay and cachexia

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Myoferlin, a candidate gene and potential modifier of muscular dystrophy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Making sense of the limb-girdle muscular dystrophies

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlin is a plasma membrane protein and is expressed early in human development

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlin, a novel skeletal muscle gene, is mutated in Miyoshi myopathy and limb girdle muscular dystrophy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Miyoshi-type distal muscular dystrophy. Clinical spectrum in 24 Dutch patients

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Myogenic cell lines derived from transgenic mice carrying a thermolabile T antigen: a model system for the derivation of tissue-specific and mutation-specific cell lines

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

A gene for autosomal recessive limb-girdle muscular dystrophy maps to chromosome 2p

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Muscle membrane repair and inflammatory attack in dysferlinopathy.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Role of thrombospondin 1 in macrophage inflammation in dysferlin myopathy.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Absence of dysferlin alters myogenin expression and delays human muscle differentiation "in vitro".

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Disruption of muscle membrane and phenotype divergence in two novel mouse models of dysferlin deficiency

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlinopathy (LGMD2B): a 23-year follow-up study of 10 patients homozygous for the same frameshifting dysferlin mutations.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Dysferlin deletion in SJL mice (SJL-Dysf) defines a natural model for limb girdle muscular dystrophy 2B

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4147957

Intrinsic differences in MyoD and myogenin expression between primary cultures of SJL/J and BALB/C skeletal muscle

28 October 2018

1 reference

12 December 2020

Spontaneous myopathy in the SJL/J mouse: pathology and strength loss

1 reference

12 December 2020

Histological assessment of SJL/J mice treated with the antioxidants coenzyme Q10 and resveratrol

1 reference

12 December 2020

The genotype of bone marrow-derived inflammatory cells does not account for differences in skeletal muscle regeneration between SJL/J and BALB/c mice

1 reference

12 December 2020

Muscle pathology in dysferlin deficiency

1 reference

12 December 2020

10.1016/J.NMD.2012.03.002

Identifiers

DOI

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31 July 2017

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31 July 2017

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