(Q55981632)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

review article

1 reference

title

Mitochondrial dysfunction in neurodegenerative diseases (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

1 reference

1 reference

M F Beal

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

publication date

1 August 1998

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

Biochimica et Biophysica Acta

3 December 2019

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

volume

1366

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

issue

1-2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

3 December 2019

page(s)

211-223

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9714810%20AND%20SRC:MED&resulttype=core&format=json

Prevalence of Alzheimer's disease in a community population of older persons. Higher than previously reported.

3 December 2019

cites work

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Increased risk of dementia in mothers of Alzheimer's disease cases: evidence for maternal inheritance

7 January 2021

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A comparison of familial and sporadic Alzheimer's disease

7 January 2021

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Metabolic reduction in the posterior cingulate cortex in very early Alzheimer's disease

7 January 2021

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Deficits in cerebral glucose metabolism demonstrated by positron emission tomography in individuals at risk of familial Alzheimer's disease

7 January 2021

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Preclinical evidence of Alzheimer's disease in persons homozygous for the epsilon 4 allele for apolipoprotein E.

7 January 2021

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Intermediary metabolism disturbance in AD/SDAT and its relation to molecular events

7 January 2021

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Mitochondrial function in brain tissue in primary degenerative dementia.

7 January 2021

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Changes in brain membrane phospholipid and high-energy phosphate metabolism precede dementia

7 January 2021

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In vivo 31P NMR profiles of Alzheimer's disease and multiple subcortical infarct dementia.

7 January 2021

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Frontal lobe phosphorus metabolism and neuropsychological function in aging and in alzheimer's disease

7 January 2021

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Abnormalities of the electron transport chain in idiopathic Parkinson's disease

7 January 2021

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No evidence for reduced thrombocyte cytochrome oxidase activity in Alzheimer's disease

7 January 2021

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Electron transport chain defects in Alzheimer's disease brain

7 January 2021

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Cortical cytochrome oxidase activity is reduced in Alzheimer's disease.

7 January 2021

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Brain Cytochrome Oxidase in Alzheimer's Disease

7 January 2021

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Human cells lacking mtDNA: repopulation with exogenous mitochondria by complementation

7 January 2021

1 reference

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Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Cybrids in Alzheimer's disease: a cellular model of the disease?

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Calcium homeostasis and reactive oxygen species production in cells transformed by mitochondria from individuals with sporadic Alzheimer's disease.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Internal Ca2+ mobilization is altered in fibroblasts from patients with Alzheimer disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Inositol phosphates and intracellular calcium after bradykinin stimulation in fibroblasts from young, normal aged and Alzheimer donors

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Calcium stores in cultured fibroblasts and their changes with Alzheimer's disease.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Elevation of plasma nitric oxide end products during focal cerebral ischemia and reperfusion in the rat.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Abnormal calcium homeostasis and mitochondrial polarization in a human encephalomyopathy

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidative damage to mitochondrial DNA is increased in Alzheimer's disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Aging, energy, and oxidative stress in neurodegenerative diseases.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Brain Regional Correspondence Between Alzheimer's Disease Histopathology and Biomarkers of Protein Oxidation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidative damage in Alzheimer's

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Widespread peroxynitrite-mediated damage in Alzheimer's disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Glycated tau protein in Alzheimer disease: a mechanism for induction of oxidant stress

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Expression of heme oxygenase-1 in the senescent and Alzheimer-diseased brain

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Effect of energy shortage and oxidative stress on amyloid precursor protein metabolism in COS cells.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidative stress increases production of beta-amyloid precursor protein and beta-amyloid (Abeta) in mammalian lenses, and Abeta has toxic effects on lens epithelial cells.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Apoptosis and increased generation of reactive oxygen species in Down's syndrome neurons in vitro.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Amyloidogenicity of rodent and human beta A4 sequences

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

In situ labeling of dying cortical neurons in normal aging and in Alzheimer's disease: correlations with senile plaques and disease progression

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidation of cysteine-322 in the repeat domain of microtubule-associated protein tau controls the in vitro assembly of paired helical filaments

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Phosphatase resistance of ERK2 brain kinase PK40erk2

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Compromised mitochondrial function leads to increased cytosolic calcium and to activation of MAP kinases

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Studies of human, mouse and yeast homologues indicate a mitochondrial function for frataxin

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Frataxin gene of Friedreich's ataxia is targeted to mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Respiratory deficiency due to loss of mitochondrial DNA in yeast lacking the frataxin homologue

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Ataxia with isolated vitamin E deficiency is caused by mutations in the alpha-tocopherol transfer protein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

alpha-Tocopherol transfer protein gene: exon skipping of all transcripts causes ataxia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Friedreich-like ataxia with retinitis pigmentosa caused by the His101Gln mutation of the alpha-tocopherol transfer protein gene

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Structural and functional brain imaging in Friedreich's ataxia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Glucose metabolism alterations in Friedreich's ataxia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Immunoreactive levels of alpha-ketoglutarate dehydrogenase subunits in Friedreich's ataxia and spinocerebellar ataxia type 1.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Superoxide dismutase concentration and activity in familial amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Mutations in copper-zinc superoxide dismutase that cause amyotrophic lateral sclerosis alter the zinc binding site and the redox behavior of the protein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Pathological implications of nitric oxide, superoxide and peroxynitrite formation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

A familial amyotrophic lateral sclerosis-associated A4V Cu, Zn-superoxide dismutase mutant has a lower Km for hydrogen peroxide. Correlation between clinical severity and the Km value.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Increased 3-nitrotyrosine and oxidative damage in mice with a human copper/zinc superoxide dismutase mutation.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superox

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Expression of a Cu,Zn superoxide dismutase typical of familial amyotrophic lateral sclerosis induces mitochondrial alteration and increase of cytosolic Ca2+ concentration in transfected neuroblastoma SH-SY5Y cells

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Cortical motor-sensory hypometabolism in amyotrophic lateral sclerosis: a PET study

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Lowered cerebral glucose utilization in amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Amyotrophic lateral sclerosis: oxidative energy metabolism and calcium homeostasis in peripheral blood lymphocytes

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Ultrastructural evidence for altered calcium in motor nerve terminals in amyotropic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Impairment of fast axonal transport in the proximal axons of anterior horn neurons in amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Ultrastructure of swollen proximal axons of anterior horn neurons in motor neuron disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Functional and morphometric study of the liver in motor neuron disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidative damage to protein in sporadic motor neuron disease spinal cord

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Decreased zinc affinity of amyotrophic lateral sclerosis-associated superoxide dismutase mutants leads to enhanced catalysis of tyrosine nitration by peroxynitrite

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Inactivation of the mouse Huntington's disease gene homolog Hdh

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Evidence for impairment of energy metabolism in vivo in Huntington's disease using localized 1H NMR spectroscopy

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Decreased N-acetyl-aspartate/choline ratio and increased lactate in the frontal lobe of patients with Huntington's disease: a proton magnetic resonance spectroscopy study

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Energy metabolism defects in Huntington's disease and effects of coenzyme Q10.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Elevated cerebrospinal fluid lactate/pyruvate ratio in Machado-Joseph disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Distribution of phosphate-activated glutaminase, succinic dehydrogenase, pyruvate dehydrogenase and gamma-glutamyl transpeptidase in post-mortem brain from Huntington's disease and agonal cases

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Biochemical abnormalities in Huntington's chorea brains

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Mitochondrial defect in Huntington's disease caudate nucleus

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Mutation of a nuclear succinate dehydrogenase gene results in mitochondrial respiratory chain deficiency

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Chronic mitochondrial energy impairment produces selective striatal degeneration and abnormal choreiform movements in primates

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Huntingtin and DRPLA proteins selectively interact with the enzyme GAPDH.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

S-Methylthiocitrulline, a neuronal nitric oxide synthase inhibitor, protects against malonate and MPTP neurotoxicity

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Huntington's disease, energy, and excitotoxicity

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

3-Nitropropionic acid-exogenous animal neurotoxin and possible human striatal toxin.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Chronic 3-nitropropionic acid treatment in baboons replicates the cognitive and motor deficits of Huntington's disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Ubiquinone protects cultured neurons against spontaneous and excitotoxin-induced degeneration

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Coenzyme Q10 attenuates the 1-methyl-4-phenyl-1,2,3,tetrahydropyridine (MPTP) induced loss of striatal dopamine and dopaminergic axons in aged mice

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Striatal malonate lesions are attenuated in neuronal nitric oxide synthase knockout mice.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Functional aspects of creatine kinase in brain.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Energy metabolism and quantal acetylcholine release: effects of botulinum toxin, 1-fluoro-2,4-dinitrobenzene, and diamide in the Torpedo electric organ

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

'Hot spots' of creatine kinase localization in brain: cerebellum, hippocampus and choroid plexus

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Phosphocreatine synthesis by isolated rat skeletal muscle mitochondria is not dependent upon external ADP: a 31P NMR study

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Phosphocreatine-dependent Glutamate Uptake by Synaptic Vesicles

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

Superoxide dismutase catalyzes nitration of tyrosines by peroxynitrite in the rod and head domains of neurofilament-L.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5

An assessment of oxidative damage to proteins, lipids, and DNA in brain from patients with Alzheimer's disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2728%2898%2900114-5