Chemical chaperones reduce endoplasmic reticulum stress and prevent mutant HFE aggregate formation (Q40108203)

17 September 2017

title

Chemical chaperones reduce endoplasmic reticulum stress and prevent mutant HFE aggregate formation (English)

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17 September 2017

main subject

endoplasmic reticulum

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17 September 2017

Maria do Carmo Fonseca

series ordinal

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17 September 2017

Jorge E Azevedo

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Maria de Sousa

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Gonçalo Picarote

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17 September 2017

John V Fleming

series ordinal

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17 September 2017

language of work or name

English

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publication date

11 July 2007

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Journal of Biological Chemistry

17 September 2017

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inferred from page(s)

published in

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17 September 2017

volume

282

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17 September 2017

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17 September 2017

page(s)

27905-27912

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A novel MHC class I-like gene is mutated in patients with hereditary haemochromatosis

17 September 2017

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21 January 2018

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XBP1 mRNA is induced by ATF6 and spliced by IRE1 in response to ER stress to produce a highly active transcription factor

21 January 2018

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Human cytomegalovirus protein US2 interferes with the expression of human HFE, a nonclassical class I major histocompatibility complex molecule that regulates iron homeostasis

21 January 2018

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21 January 2018

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Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency

21 January 2018

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21 January 2018

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Chemical chaperones reduce ER stress and restore glucose homeostasis in a mouse model of type 2 diabetes

21 January 2018

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Common structure and toxic function of amyloid oligomers implies a common mechanism of pathogenesis

21 January 2018

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Protofibrils, pores, fibrils, and neurodegeneration: separating the responsible protein aggregates from the innocent bystanders

21 January 2018

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Molecular chaperones and protein quality control

21 January 2018

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Molecular chaperones as modulators of polyglutamine protein aggregation and toxicity

21 January 2018

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Suppressive effects of 4-phenylbutyrate on the aggregation of Pael receptors and endoplasmic reticulum stress

21 January 2018

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21 January 2018

Identifiers

DOI

10.1074/JBC.M702672200

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17 September 2017

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