Cystathionine gamma-Lyase-deficient mice require dietary cysteine to protect against acute lethal myopathy and oxidative injury. (Q30496159)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566639%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

title

Cystathionine gamma-Lyase-deficient mice require dietary cysteine to protect against acute lethal myopathy and oxidative injury (English)

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6 February 2020

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6 February 2020

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6 February 2020

Noriyuki Akahoshi

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6 February 2020

Hidenori Yamada

series ordinal

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6 February 2020

Shintaro Nakano

series ordinal

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6 February 2020

Takashi Izumi

series ordinal

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6 February 2020

language of work or name

English

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publication date

21 June 2010

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Journal of Biological Chemistry

6 February 2020

published in

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6 February 2020

volume

285

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6 February 2020

issue

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6 February 2020

page(s)

26358-26368

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Muscle inactivation of mTOR causes metabolic and dystrophin defects leading to severe myopathy

6 February 2020

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Genomic basis of cystathioninuria (MIM 219500) revealed by multiple mutations in cystathionine gamma-lyase (CTH).

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14 July 2018

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14 July 2018

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14 July 2018

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14 July 2018

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14 July 2018

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14 July 2018

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Impairment of cysteine synthesis from methionine in rats exposed to surgical stress

14 July 2018

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Cystathionine beta-synthase as a carbon monoxide-sensitive regulator of bile excretion

14 July 2018

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Hyperhomocysteinemia accelerates atherosclerosis in cystathionine beta-synthase and apolipoprotein E double knock-out mice with and without dietary perturbation

21 January 2018

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Abnormal lipid metabolism in cystathionine beta-synthase-deficient mice, an animal model for hyperhomocysteinemia.

21 January 2018

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Genetic background conversion ameliorates semi-lethality and permits behavioral analyses in cystathionine beta-synthase-deficient mice, an animal model for hyperhomocysteinemia

21 January 2018

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Elevated plasma total homocysteine in severe methionine adenosyltransferase I/III deficiency

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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26 November 2018

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12 December 2020

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12 December 2020

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12 December 2020

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Effects of age on levels of cysteine, glutathione and related enzyme activities in livers of mice and rats and an attempt to replenish hepatic glutathione level of mouse with cysteine derivatives

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12 December 2020

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12 December 2020

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12 December 2020

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Identifiers

DOI

10.1074/JBC.M110.147439

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566639%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566639%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

PubMed publication ID

20566639

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566639%20AND%20SRC:MED&resulttype=core&format=json