Oxidative stress in phenylketonuria: what is the evidence? (Q37868451)

24 August 2017

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title

Oxidative stress in phenylketonuria: what is the evidence? (English)

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24 August 2017

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Moacir Wajner

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24 August 2017

Graziela S Ribas

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24 August 2017

Angela Sitta

series ordinal

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24 August 2017

Carmen R Vargas

series ordinal

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24 August 2017

publication date

23 April 2011

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Cellular and Molecular Neurobiology

24 August 2017

published in

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24 August 2017

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24 August 2017

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24 August 2017

page(s)

653-662

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Oxidative stress in neurodegeneration: cause or consequence?

24 August 2017

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Hyperphenylalaninemia reduces creatine kinase activity in the cerebral cortex of rats

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Protein carbonyl groups as biomarkers of oxidative stress.

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Glutaric acid induces oxidative stress in brain of young rats

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Mitochondrial function as a determinant of recovery or death in cell response to injury.

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A review of recent studies on the metabolism of exogenous and endogenous malondialdehyde

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Reactive carbonyls and oxidative stress: potential for therapeutic intervention

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21 January 2018

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Chemistry and biochemistry of 4-hydroxynonenal, malonaldehyde and related aldehydes

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Free radicals, antioxidants, and nutrition

21 January 2018

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Alanine prevents the reduction of pyruvate kinase activity in brain cortex of rats subjected to chemically induced hyperphenylalaninemia.

21 January 2018

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Experimental evidence that phenylalanine provokes oxidative stress in hippocampus and cerebral cortex of developing rats

21 January 2018

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Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats.

21 January 2018

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Superoxide radical and superoxide dismutases

21 January 2018

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Fundamental aspects of reactive oxygen species, or what's the matter with oxygen?

21 January 2018

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Cognitive functions and the antioxidant system in phenylketonuric patients

21 January 2018

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Phenylketonuria: dietary and therapeutic challenges

21 January 2018

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Antioxidant and antiradical activities of L-carnitine

21 January 2018

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Role of free radicals in the neurodegenerative diseases: therapeutic implications for antioxidant treatment

21 January 2018

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Oxidative stress and neurodegeneration: where are we now?

21 January 2018

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"Hypotyrosinemia" in phenylketonuria

21 January 2018

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Cerebral Glucose Metabolism Is Decreased in White Matter Changes in Patients with Phenylketonuria

21 January 2018

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Quantification of protein modification by oxidants

21 January 2018

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Biological selectivity and functional aspects of protein tyrosine nitration

21 January 2018

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Oxidative stress and the pathogenesis of Parkinson's disease

21 January 2018

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Non-linear accumulation of 8-hydroxy-2'-deoxyguanosine, a marker of oxidized DNA damage, during aging

21 January 2018

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Experimental hyperphenylalaninemia provokes oxidative stress in rat brain.

21 January 2018

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Biochemical and neuropsychological effects of elevated plasma phenylalanine in patients with treated phenylketonuria. A model for the study of phenylalanine and brain function in man

21 January 2018

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Clinical and nutritional evaluation of phenylketonuric patients on tetrahydrobiopterin monotherapy.

21 January 2018

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3-Hydroxyglutaric acid induces oxidative stress and decreases the antioxidant defenses in cerebral cortex of young rats

21 January 2018

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Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats.

21 January 2018

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Carbonyl modified proteins in cellular regulation, aging, and disease

21 January 2018

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21 January 2018

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Oxidative stress induced by phenylketonuria in the rat: Prevention by melatonin, vitamin E, and vitamin C.

21 January 2018

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21 January 2018

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Novel mechanisms of natural antioxidant compounds in biological systems: involvement of glutathione and glutathione-related enzymes

21 January 2018

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The evolution of free radicals and oxidative stress

21 January 2018

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Transition metals as catalysts of "autoxidation" reactions

21 January 2018

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The L-arginine-nitric oxide pathway

21 January 2018

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Lipoic acid prevents oxidative stress in vitro and in vivo by an acute hyperphenylalaninemia chemically-induced in rat brain

21 January 2018

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The effect of hyperphenylalaninemia on size and density of synapses in rat neocortex

21 January 2018

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Lipid peroxidation: physiological levels and dual biological effects

21 January 2018

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Adventiously-bound redox active iron and copper are at the center of oxidative damage in Alzheimer disease

21 January 2018

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Neurological aspects of adult phenylketonuria

21 January 2018

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Nutrition, physical growth, and bone density in treated phenylketonuria

21 January 2018

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Inhibition of the mitochondrial respiratory chain by phenylalanine in rat cerebral cortex

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress and the pathogenesis of neurodegenerative disorders

21 January 2018

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Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of L-carnitine supplementation

21 January 2018

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Methylmalonic acidaemia leads to increased production of reactive oxygen species and induction of apoptosis through the mitochondrial/caspase pathway

21 January 2018

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Biophysical consequences of lipid peroxidation in membranes

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of phenylalanine, p-chlorophenylalanine and alpha-methylphenylalanine on glucose uptake in vitro by the brain of young rats

21 January 2018

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Effect of diet on plasma total antioxidant status in phenylketonuric patients

21 January 2018

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Low total antioxidant status is implicated with high 8-hydroxy-2-deoxyguanosine serum concentrations in phenylketonuria

21 January 2018

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Lipid composition of human cerebral white matter and myelin in phenylketonuria

21 January 2018

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Oxidative stress in patients with phenylketonuria.

21 January 2018

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Investigation of oxidative stress parameters in treated phenylketonuric patients.

21 January 2018

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Evidence that DNA damage is associated to phenylalanine blood levels in leukocytes from phenylketonuric patients

21 January 2018

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L-carnitine blood levels and oxidative stress in treated phenylketonuric patients

21 January 2018

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Effect of short- and long-term exposition to high phenylalanine blood levels on oxidative damage in phenylketonuric patients.

21 January 2018

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Behaviour in early treated phenylketonuria: a systematic review

21 January 2018

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Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.

21 January 2018

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Inhibition of rat brain Na+, K+-ATPase activity induced by homocysteine is probably mediated by oxidative stress.

21 January 2018

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In vitro effect of homocysteine on some parameters of oxidative stress in rat hippocampus

21 January 2018

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Biochemical markers related to Alzheimer's dementia in serum and cerebrospinal fluid

21 January 2018

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4-Hydroxy-2-nonenal: a product and mediator of oxidative stress

21 January 2018

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Effect of experimental hyperphenylalaninemia on the postnatal rat brain.

21 January 2018

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Role of oxygen radicals in DNA damage and cancer incidence.

21 January 2018

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Free radicals and antioxidants in normal physiological functions and human disease

21 January 2018

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The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies.

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Selenium, glutathione peroxidase (GSH-Px) and lipid peroxidation products before and after selenium supplementation

21 January 2018

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Alanine prevents the decrease of Na+,K+-ATPase activity in experimental phenylketonuria.

21 January 2018

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Inhibition of Na(+),K(+)-ATPase activity in hippocampus of rats subjected to acute administration of homocysteine is prevented by vitamins E and C treatment

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Redox sensing by prokaryotic transcription factors

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of L-Carnitine derivatives on heart mitochondrial damage induced by lipid peroxidation

21 January 2018

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Oxidative stress in the context of acute cerebrovascular stroke

21 January 2018

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12 December 2020

L-propionyl carnitine protects erythrocytes and low density lipoproteins against peroxidation

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12 December 2020

Antioxidant status in hyperphenylalaninemia

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12 December 2020

Thought processes as related to brain metabolism in certain abnormal conditions.

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12 December 2020

Chromatographic determination of 8-oxo-7,8-dihydro-2'-deoxyguanosine in cellular DNA: a validation study

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12 December 2020

Plasma selenium levels in treated phenylketonuric patients

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12 December 2020

The roles of free radicals in amyotrophic lateral sclerosis: reactive oxygen species and elevated oxidation of protein, DNA, and membrane phospholipids

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12 December 2020

Alanine reverses the inhibitory effect of phenylalanine and its metabolites on Na+,K+-ATPase in synaptic plasma membranes from cerebral cortex of rats

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12 December 2020

Lipophilic antioxidants in patients with phenylketonuria

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12 December 2020

Decreased serum ubiquinone-10 concentrations in phenylketonuria

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12 December 2020

The comet assay: a comprehensive review

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12 December 2020

Serotonin and Dopamine Synthesis in Phenylketonuria

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12 December 2020

Erythrocyte glutathione peroxidase activity and plasma selenium concentration are reduced in maple syrup urine disease patients during treatment

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12 December 2020

Effect of phenylalanine and alpha-methylphenylalanine on in vitro incorporation of 32P into cytoskeletal cerebral proteins

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12 December 2020

Mitochondrial damage: an important feature in a number of inborn errors of metabolism?

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12 December 2020

Tocopherol in inborn errors of intermediary metabolism

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12 December 2020

Evaluation of total antioxidant potential (TRAP) and total antioxidant reactivity from luminol-enhanced chemiluminescence measurements

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12 December 2020

Protein status of infants with phenylketonuria undergoing nutrition management

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12 December 2020

Trace element nutrition status and dietary intake of children with phenylketonuria

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12 December 2020

Antioxidant and thyroid hormone status in selenium-deficient phenylketonuric and hyperphenylalaninemic patients

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12 December 2020

Plasma glutathione peroxidase after selenium supplementation in patients with reduced selenium state

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12 December 2020

Plasma antioxidant capacity in two cases of tyrosinaemia type 1: one case treated with NTBC

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12 December 2020

Serum selenium levels in individuals on PKU diets

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12 December 2020

Dietary interventions for phenylketonuria

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12 December 2020

Micronutrients: oxidant/antioxidant status.

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12 December 2020

Coenzyme Q10 in the diet-daily intake and relative bioavailability

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12 December 2020

Serum carnitine level in phenylketonuric children under dietary control in Greece

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12 December 2020

[Congenital errors of metabolism: cause of oxidative stress?]

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12 December 2020

Neurological findings in early treated phenylketonuria

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12 December 2020

10.1007/S10571-011-9693-2

Identifiers

DOI

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24 August 2017

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