Filipin recognizes both GM1 and cholesterol in GM1 gangliosidosis mouse brain (Q35067305)

6 August 2017

title

Filipin recognizes both GM1 and cholesterol in GM1 gangliosidosis mouse brain (English)

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6 August 2017

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6 August 2017

Julian R Arthur

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6 August 2017

Karie A Heinecke

series ordinal

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6 August 2017

publication date

20 April 2011

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Journal of Lipid Research

6 August 2017

published in

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6 August 2017

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6 August 2017

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6 August 2017

page(s)

1345-1351

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describes a project that uses

6 August 2017

ImageQuant

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3122916/fullTextXML

inferred from PubMed Central ID database lookup

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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An electrophoretic variant of beta-galactosidase with altered catalytic properties in a patient with GM1 gangliosidosis

8 July 2018

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Complete correction of enzymatic deficiency and neurochemistry in the GM1-gangliosidosis mouse brain by neonatal adeno-associated virus-mediated gene delivery

8 July 2018

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Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice.

27 September 2018

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27 September 2018

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27 September 2018

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27 September 2018

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Cholesterol accumulation in NPC1-deficient neurons is ganglioside dependent

27 September 2018

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Sphingolipid storage induces accumulation of intracellular cholesterol by stimulating SREBP-1 cleavage

27 September 2018

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Filipin III: Configuration Assignment and Confirmation by Synthetic Correlation

27 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Quantified increases of cholesterol, total lipid and globotriaosylceramide in filipin-positive Niemann-Pick type C fibroblasts

27 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Jamming the endosomal system: lipid rafts and lysosomal storage diseases.

27 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Cholesterol modulates membrane traffic along the endocytic pathway in sphingolipid-storage diseases

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Increased levels of GM2 ganglioside in fibroblasts from a patient with juvenile Niemann-Pick disease type C.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Filipin, an Antifungal Antibiotic: Isolation and Properties

27 September 2018

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Crossref

https://api.crossref.org/works/10.1194%2FJLR.M012633

GM1-ganglioside-mediated activation of the unfolded protein response causes neuronal death in a neurodegenerative gangliosidosis

21 January 2018

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12 December 2020

Filipin as a cholesterol probe. I. Morphology of filipin-cholesterol interaction in lipid model systems

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12 December 2020

Filipin as a fluorescent probe of lipoprotein-derived sterols on thin-layer chromatograms

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12 December 2020

Distinct alterations in phospholipid metabolism in brains of apolipoprotein E-deficient mice

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12 December 2020

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis

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12 December 2020

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12 December 2020

Oxidation products of cholesteryl linoleate are resistant to hydrolysis in macrophages, form complexes with proteins, and are present in human atherosclerotic lesions

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12 December 2020

Generalized CNS disease and massive GM1-ganglioside accumulation in mice defective in lysosomal acid beta-galactosidase

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12 December 2020

Lipid Composition of Whole Brain and Cerebellum in Hurler Syndrome (MPS IH) Mice

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12 December 2020

Identifiers

DOI

10.1194/JLR.M012633

1 reference

6 August 2017

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6 August 2017

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