Corticospinal Motor Neurons Are Susceptible to Increased ER Stress and Display Profound Degeneration in the Absence of UCHL1 Function (Q27302932)

25596590

26 June 2017

title

Corticospinal Motor Neurons Are Susceptible to Increased ER Stress and Display Profound Degeneration in the Absence of UCHL1 Function (English)

1 reference

26 June 2017

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25596590%20AND%20SRC:MED&resulttype=core&format=json

31 May 2020

Barış Genç

1 reference

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31 May 2020

Gregory A Cox

1 reference

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31 May 2020

Martha C Bohn

1 reference

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31 May 2020

Raymond P Roos

1 reference

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31 May 2020

Jeffrey D Macklis

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31 May 2020

Emel Ulupınar

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31 May 2020

P Hande Özdinler

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31 May 2020

language of work or name

English

0 references

publication date

16 January 2015

1 reference

26 June 2017

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31 May 2020

volume

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31 May 2020

issue

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31 May 2020

page(s)

4259-4272

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Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia

31 May 2020

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Could dysregulation of UPS be a common underlying mechanism for cancer and neurodegeneration? Lessons from UCHL1.

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eGFP expression under UCHL1 promoter genetically labels corticospinal motor neurons and a subpopulation of degeneration-resistant spinal motor neurons in an ALS mouse model

28 September 2017

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Recessive loss of function of the neuronal ubiquitin hydrolase UCHL1 leads to early-onset progressive neurodegeneration

28 September 2017

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UCHL1 regulates ubiquitination and recycling of the neural cell adhesion molecule NCAM.

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28 September 2017

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28 September 2017

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28 September 2017

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28 September 2017

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28 September 2017

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28 September 2017

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31 May 2018

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31 May 2018

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31 May 2018

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Ubiquitin carboxyl-terminal hydrolase (PGP 9.5) is selectively present in ubiquitinated inclusion bodies characteristic of human neurodegenerative diseases

31 May 2018

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31 May 2018

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Oxidative modifications and down-regulation of ubiquitin carboxyl-terminal hydrolase L1 associated with idiopathic Parkinson's and Alzheimer's diseases

21 January 2018

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Ubiquitin C-terminal hydrolase-L1 interacts with adhesion complexes and promotes cell migration, survival, and anchorage independent growth.

21 January 2018

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Pharmacological reduction of ER stress protects against TDP-43 neuronal toxicity in vivo.

21 January 2018

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Ubiquitin-positive inclusions and progression of pathology in frontotemporal dementia and motor neurone disease identifies a group with mainly early pathology

21 January 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/25596590

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/25596590

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Ubiquitin, cellular inclusions and their role in neurodegeneration

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/25596590

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1093/CERCOR/BHU318

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25596590%20AND%20SRC:MED&resulttype=core&format=json

OpenCitations bibliographic resource ID

31 May 2020

4135753

1 reference

Consolidated OpenCitations Corpus – April 2017

OpenCitations bibliographic resource ID

2 references

Consolidated OpenCitations Corpus – April 2017

OpenCitations bibliographic resource ID

4135753

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25596590%20AND%20SRC:MED&resulttype=core&format=json

31 May 2020

25596590

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25596590%20AND%20SRC:MED&resulttype=core&format=json