The human mitochondrial transcriptome and the RNA-binding proteins that regulate its expression (Q27016551)

Distinctive features of the 5'-terminal sequences of the human mitochondrial mRNAs

21 January 2018

1 reference

tRNA punctuation model of RNA processing in human mitochondria

21 January 2018

1 reference

Long noncoding RNAs are generated from the mitochondrial genome and regulated by nuclear-encoded proteins

21 January 2018

1 reference

The human mitochondrial transcriptome

21 January 2018

1 reference

The genetics and pathology of oxidative phosphorylation

21 January 2018

1 reference

Symmetrical In Vivo Transcription of Mitochondrial DNA in HeLa Cells

21 January 2018

1 reference

Identification of initiation sites for heavy-strand and light-strand transcription in human mitochondrial DNA

21 January 2018

1 reference

A tridecamer DNA sequence supports human mitochondrial RNA 3'-end formation in vitro

21 January 2018

1 reference

Initiation and beyond: multiple functions of the human mitochondrial transcription machinery

21 January 2018

1 reference

DNA replication and transcription in mammalian mitochondria

21 January 2018

1 reference

Mitochondrial DNA replication and repair: all a flap

21 January 2018

1 reference

Mitochondrial DNA maintenance in vertebrates

21 January 2018

1 reference

The human mitochondrial replication fork in health and disease

21 January 2018

1 reference

RNase P without RNA: identification and functional reconstitution of the human mitochondrial tRNA processing enzyme

21 January 2018

1 reference

Involvement of human ELAC2 gene product in 3' end processing of mitochondrial tRNAs

21 January 2018

1 reference

RNA processing in human mitochondria

21 January 2018

1 reference

Nuclear genetic defects of oxidative phosphorylation

21 January 2018

1 reference

A different genetic code in human mitochondria

21 January 2018

1 reference

Human mitochondrial mRNAs--like members of all families, similar but different

21 January 2018

1 reference

Polyadenylation and degradation of human mitochondrial RNA: the prokaryotic past leaves its mark

21 January 2018

1 reference

Polyadenylation and degradation of mRNA in mammalian mitochondria: a missing link?

21 January 2018

1 reference

RNA turnover in human mitochondria: more questions than answers?

21 January 2018

1 reference

Messenger RNA stability in mitochondria: different means to an end.

21 January 2018

1 reference

Polyadenylation in mammalian mitochondria: insights from recent studies.

21 January 2018

1 reference

Hungry codons promote frameshifting in human mitochondrial ribosomes

21 January 2018

1 reference

Targeting of the cytosolic poly(A) binding protein PABPC1 to mitochondria causes mitochondrial translation inhibition

21 January 2018

1 reference

PDE12 removes mitochondrial RNA poly(A) tails and controls translation in human mitochondria

21 January 2018

1 reference

LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs

21 January 2018

1 reference

Molecular dysfunction associated with the human mitochondrial 3302A>G mutation in the MTTL1 (mt-tRNALeu(UUR)) gene

21 January 2018

1 reference

Human mitochondrial RNA turnover caught in flagranti: involvement of hSuv3p helicase in RNA surveillance

21 January 2018

1 reference

Structure of transfer RNAs: similarity and variability

21 January 2018

1 reference

Mitochondrial tRNA 3' end metabolism and human disease.

21 January 2018

1 reference

Search for characteristic structural features of mammalian mitochondrial tRNAs.

21 January 2018

1 reference

Human mitochondrial tRNAs: biogenesis, function, structural aspects, and diseases

21 January 2018

1 reference

tRNA Modification and Genetic Code Variations in Animal Mitochondria

21 January 2018

1 reference

Identification and characterization of mammalian mitochondrial tRNA nucleotidyltransferases

21 January 2018

1 reference

A eubacterial origin for the human tRNA nucleotidyltransferase?

21 January 2018

1 reference

Global identification of microRNA-target RNA pairs by parallel analysis of RNA ends

21 January 2018

1 reference

Proteomic analysis of the mammalian mitochondrial ribosome. Identification of protein components in the 28 S small subunit

21 January 2018

1 reference

Structural compensation for the deficit of rRNA with proteins in the mammalian mitochondrial ribosome. Systematic analysis of protein components of the large ribosomal subunit from mammalian mitochondria

21 January 2018

1 reference

A structural model for the large subunit of the mammalian mitochondrial ribosome.

21 January 2018

1 reference

Structure of the Mammalian Mitochondrial Ribosome Reveals an Expanded Functional Role for Its Component Proteins

21 January 2018

1 reference

Identification of small non-coding RNAs from mitochondria and chloroplasts

21 January 2018

1 reference

Expression of a novel non-coding mitochondrial RNA in human proliferating cells.

21 January 2018

1 reference

Disruption of a mitochondrial RNA-binding protein gene results in decreased cytochrome b expression and a marked reduction in ubiquinol-cytochrome c reductase activity in mouse heart mitochondria

21 January 2018

1 reference

Mitochondrial transcription factors B1 and B2 activate transcription of human mtDNA

21 January 2018

1 reference

Architectural role of mitochondrial transcription factor A in maintenance of human mitochondrial DNA

21 January 2018

1 reference

In Arabidopsis thaliana, 1% of the genome codes for a novel protein family unique to plants

21 January 2018

1 reference

The PPR motif - a TPR-related motif prevalent in plant organellar proteins

21 January 2018

1 reference

Structure of human mitochondrial RNA polymerase

21 January 2018

1 reference

Multiple interactions involving the amino-terminal domain of yeast mtRNA polymerase determine the efficiency of mitochondrial protein synthesis

21 January 2018

1 reference

Stability of the mitochondrial genome requires an amino-terminal domain of yeast mitochondrial RNA polymerase

21 January 2018

1 reference

TEFM (c17orf42) is necessary for transcription of human mtDNA

21 January 2018

1 reference

tRNA recognition, processing, and disease: hypotheses around an unorthodox type of RNase P in human mitochondria

21 January 2018

1 reference

Processing mitochondrial (t)RNAs: new enzyme, old job.

21 January 2018

1 reference

Multiple functions of type 10 17beta-hydroxysteroid dehydrogenase

21 January 2018

1 reference

A single Arabidopsis organellar protein has RNase P activity.

21 January 2018

1 reference

Localization of human RNase Z isoforms: dual nuclear/mitochondrial targeting of the ELAC2 gene product by alternative translation initiation

21 January 2018

1 reference

A candidate prostate cancer susceptibility gene at chromosome 17p

21 January 2018

1 reference

A candidate prostate cancer susceptibility gene encodes tRNA 3' processing endoribonuclease

21 January 2018

1 reference

Pentatricopeptide repeat domain protein 1 lowers the levels of mitochondrial leucine tRNAs in cells

21 January 2018

1 reference

RNA processing in a tiny transcriptome.

21 January 2018

1 reference

Aminoacyl-tRNA synthetases

21 January 2018

1 reference

C to U editing and modifications during the maturation of the mitochondrial tRNA(Asp) in marsupials

21 January 2018

1 reference

Nuclear control of cloverleaf structure of human mitochondrial tRNA(Lys).

21 January 2018

1 reference

Missense mutation in pseudouridine synthase 1 (PUS1) causes mitochondrial myopathy and sideroblastic anemia (MLASA).

21 January 2018

1 reference

Mitochondrial myopathy and sideroblastic anemia (MLASA): missense mutation in the pseudouridine synthase 1 (PUS1) gene is associated with the loss of tRNA pseudouridylation

21 January 2018

1 reference

tRNA's wobble decoding of the genome: 40 years of modification

21 January 2018

1 reference

Mitochondria-specific RNA-modifying enzymes responsible for the biosynthesis of the wobble base in mitochondrial tRNAs. Implications for the molecular pathogenesis of human mitochondrial diseases

21 January 2018

1 reference

A human mitochondrial GTP binding protein related to tRNA modification may modulate phenotypic expression of the deafness-associated mitochondrial 12S rRNA mutation

21 January 2018

1 reference

Isolation and characterization of the putative nuclear modifier gene MTO1 involved in the pathogenesis of deafness-associated mitochondrial 12 S rRNA A1555G mutation

21 January 2018

1 reference

Taurine as a constituent of mitochondrial tRNAs: new insights into the functions of taurine and human mitochondrial diseases

21 January 2018

1 reference

Human mitochondrial diseases caused by lack of taurine modification in mitochondrial tRNAs

21 January 2018

1 reference

Codon-specific translational defect caused by a wobble modification deficiency in mutant tRNA from a human mitochondrial disease

21 January 2018

1 reference

Wobble modification defect in tRNA disturbs codon-anticodon interaction in a mitochondrial disease

21 January 2018

1 reference

Synthesis and investigation of the 5-formylcytidine modified, anticodon stem and loop of the human mitochondrial tRNAMet

21 January 2018

1 reference

Unconventional decoding of the AUA codon as methionine by mitochondrial tRNAMet with the anticodon f5CAU as revealed with a mitochondrial in vitro translation system

21 January 2018

1 reference

Mammalian mitochondrial methionyl-tRNA transformylase from bovine liver. Purification, characterization, and gene structure.

21 January 2018

1 reference

Recognition of tRNAs by Methionyl-tRNA transformylase from mammalian mitochondria

21 January 2018

1 reference

Mutations in MTFMT underlie a human disorder of formylation causing impaired mitochondrial translation

21 January 2018

1 reference

Phenotype of non-syndromic deafness associated with the mitochondrial A1555G mutation is modulated by mitochondrial RNA modifying enzymes MTO1 and GTPBP3

21 January 2018

1 reference

Biochemical evidence for nuclear gene involvement in phenotype of non-syndromic deafness associated with mitochondrial 12S rRNA mutation

21 January 2018

1 reference

Mutation in TRMU related to transfer RNA modification modulates the phenotypic expression of the deafness-associated mitochondrial 12S ribosomal RNA mutations

21 January 2018

1 reference

Elucidation of separate, but collaborative functions of the rRNA methyltransferase-related human mitochondrial transcription factors B1 and B2 in mitochondrial biogenesis reveals new insight into maternally inherited deafness

21 January 2018

1 reference

Human mitochondrial transcription factor B1 methylates ribosomal RNA at a conserved stem-loop

21 January 2018

1 reference

Human mitochondrial transcription factor B1 as a modifier gene for hearing loss associated with the mitochondrial A1555G mutation

21 January 2018

1 reference

Methylation of 12S rRNA is necessary for in vivo stability of the small subunit of the mammalian mitochondrial ribosome

21 January 2018

1 reference

Something old, something new, something borrowed ...

21 January 2018

1 reference

Mitochondrial stress engages E2F1 apoptotic signaling to cause deafness

21 January 2018

1 reference

Defective mitochondrial mRNA maturation is associated with spastic ataxia

21 January 2018

1 reference

Identification of a novel human nuclear-encoded mitochondrial poly(A) polymerase

21 January 2018

1 reference

Structural basis for dimerization and activity of human PAPD1, a noncanonical poly(A) polymerase

21 January 2018

1 reference

Human polynucleotide phosphorylase: location matters

21 January 2018

1 reference

Mammalian polynucleotide phosphorylase is an intermembrane space RNase that maintains mitochondrial homeostasis

21 January 2018

1 reference

LRPPRC is a mitochondrial matrix protein that is conserved in metazoans

21 January 2018

1 reference

The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster

21 January 2018

1 reference

LRPPRC and SLIRP interact in a ribonucleoprotein complex that regulates posttranscriptional gene expression in mitochondria.

21 January 2018

1 reference

Identification of a gene causing human cytochrome c oxidase deficiency by integrative genomics

21 January 2018

1 reference

Mitochondrial and nuclear genomic responses to loss of LRPPRC expression

21 January 2018

1 reference

A computational screen for regulators of oxidative phosphorylation implicates SLIRP in mitochondrial RNA homeostasis

21 January 2018

1 reference

Human ATP-dependent RNA/DNA helicase hSuv3p interacts with the cofactor of survivin HBXIP.

21 January 2018

1 reference

Localisation of the human hSuv3p helicase in the mitochondrial matrix and its preferential unwinding of dsDNA

21 January 2018

1 reference

Human mitochondrial SUV3 and polynucleotide phosphorylase form a 330-kDa heteropentamer to cooperatively degrade double-stranded RNA with a 3'-to-5' directionality

21 January 2018

1 reference

The 2-5A/RNase L/RNase L inhibitor (RLI) [correction of (RNI)] pathway regulates mitochondrial mRNAs stability in interferon alpha-treated H9 cells

21 January 2018

1 reference

Regulation of mitochondrial mRNA stability by RNase L is translation-dependent and controls IFNalpha-induced apoptosis

21 January 2018

1 reference

Mutation in TACO1, encoding a translational activator of COX I, results in cytochrome c oxidase deficiency and late-onset Leigh syndrome.

21 January 2018

1 reference

Unilateral aminoacylation specificity between bovine mitochondria and eubacteria

21 January 2018

1 reference

Dual mode recognition of two isoacceptor tRNAs by mammalian mitochondrial seryl-tRNA synthetase.

21 January 2018

1 reference

Crystal structure of human mitochondrial tyrosyl-tRNA synthetase reveals common and idiosyncratic features

21 January 2018

1 reference

Loss of a primordial identity element for a mammalian mitochondrial aminoacylation system.

21 January 2018

1 reference

Biogenesis of glutaminyl-mt tRNAGln in human mitochondria

21 January 2018

1 reference

Human diseases with impaired mitochondrial protein synthesis

21 January 2018

1 reference

Reconstructing the evolution of the mitochondrial ribosomal proteome.

21 January 2018

1 reference

The large subunit of the mammalian mitochondrial ribosome. Analysis of the complement of ribosomal proteins present

21 January 2018

1 reference

Properties of human mitochondrial ribosomes

21 January 2018

1 reference

Mitochondrial ribosomal proteins: candidate genes for mitochondrial disease

21 January 2018

1 reference

Mitochondrial ribosomal protein L12 selectively associates with human mitochondrial RNA polymerase to activate transcription

21 January 2018

1 reference

Termination of Protein Synthesis in Mammalian Mitochondria

21 January 2018

1 reference

Translation termination in human mitochondrial ribosomes.

21 January 2018

1 reference

How do mammalian mitochondria synthesize proteins?

21 January 2018

1 reference

Unique features of animal mitochondrial translation systems. The non-universal genetic code, unusual features of the translational apparatus and their relevance to human mitochondrial diseases

21 January 2018

1 reference

Evidence for an active role of IF3mt in the initiation of translation in mammalian mitochondria

21 January 2018

1 reference

A single mammalian mitochondrial translation initiation factor functionally replaces two bacterial factors

21 January 2018

1 reference

Crystal structure of the bovine mitochondrial elongation factor Tu.Ts complex

21 January 2018

1 reference

Aminoacyl-tRNA surveillance by EF-Tu in mammalian mitochondria

21 January 2018

1 reference

EF-G2mt is an exclusive recycling factor in mammalian mitochondrial protein synthesis

21 January 2018

1 reference

mtRF1a is a human mitochondrial translation release factor decoding the major termination codons UAA and UAG

21 January 2018

1 reference

A functional peptidyl-tRNA hydrolase, ICT1, has been recruited into the human mitochondrial ribosome

21 January 2018

1 reference

Mutations in C12orf65 in patients with encephalomyopathy and a mitochondrial translation defect

21 January 2018

1 reference

The human mitochondrial ribosome recycling factor is essential for cell viability

21 January 2018

1 reference

hNOA1 interacts with complex I and DAP3 and regulates mitochondrial respiration and apoptosis

21 January 2018

1 reference

NOA1 is an essential GTPase required for mitochondrial protein synthesis

21 January 2018

1 reference

ERAL1 is associated with mitochondrial ribosome and elimination of ERAL1 leads to mitochondrial dysfunction and growth retardation

21 January 2018

1 reference

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

21 January 2018

1 reference

MTERF4 regulates translation by targeting the methyltransferase NSUN4 to the mammalian mitochondrial ribosome

21 January 2018

1 reference

C7orf30 is necessary for biogenesis of the large subunit of the mitochondrial ribosome

21 January 2018

1 reference

C7orf30 specifically associates with the large subunit of the mitochondrial ribosome and is involved in translation

21 January 2018

1 reference

Construction of Parallel Analysis of RNA Ends (PARE) libraries for the study of cleaved miRNA targets and the RNA degradome

21 January 2018

1 reference

RNA sequencing: advances, challenges and opportunities

21 January 2018

1 reference

Short non-coding RNA fragments accumulating in chloroplasts: footprints of RNA binding proteins?

21 January 2018

1 reference

Protein-mediated protection as the predominant mechanism for defining processed mRNA termini in land plant chloroplasts

21 January 2018

1 reference

Meta-analysis of small RNA-sequencing errors reveals ubiquitous post-transcriptional RNA modifications.

21 January 2018

1 reference

Traces of post-transcriptional RNA modifications in deep sequencing data

21 January 2018

1 reference

Pentatricopeptide repeat proteins: a socket set for organelle gene expression.

21 January 2018

1 reference

Genome-wide analysis of Arabidopsis pentatricopeptide repeat proteins reveals their essential role in organelle biogenesis

21 January 2018

1 reference

Genome-wide analysis of RNA-protein interactions in plants

21 January 2018

1 reference

Studying the structure and processing of chloroplast transcripts

21 January 2018

1 reference

Mechanism of RNA stabilization and translational activation by a pentatricopeptide repeat protein

21 January 2018

1 reference

In vitro RNA-binding assay for studying trans-factors for RNA editing in chloroplasts.

21 January 2018

1 reference

Selection patterns on restorer-like genes reveal a conflict between nuclear and mitochondrial genomes throughout angiosperm evolution.

21 January 2018

1 reference

Pentatricopeptide repeat (PPR) proteins as sequence-specificity factors in post-transcriptional processes in organelles

21 January 2018

1 reference

Sequence-specific binding of a chloroplast pentatricopeptide repeat protein to its native group II intron ligand.

21 January 2018

1 reference

Modular recognition of nucleic acids by PUF, TALE and PPR proteins

21 January 2018

1 reference

Revisiting the yeast PPR proteins--application of an Iterative Hidden Markov Model algorithm reveals new members of the rapidly evolving family

21 January 2018

1 reference

A genome wide study in fission yeast reveals nine PPR proteins that regulate mitochondrial gene expression

21 January 2018

1 reference

Pentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translation

21 January 2018

1 reference

The evolution of RNA editing and pentatricopeptide repeat genes.

21 January 2018

1 reference

RNA editing in plant organelles: machinery, physiological function and evolution

21 January 2018

1 reference

Pentatricopeptide Repeat Proteins Stimulate mRNA Adenylation/Uridylation to Activate Mitochondrial Translation in Trypanosomes

21 January 2018

1 reference

Identification of pentatricopeptide repeat proteins in Trypanosoma brucei

21 January 2018

1 reference

DMR1 (CCM1/YGR150C) of Saccharomyces cerevisiae encodes an RNA-binding protein from the pentatricopeptide repeat family required for the maintenance of the mitochondrial 15S ribosomal RNA.

21 January 2018

1 reference

The pentatricopeptide repeats present in Pet309 are necessary for translation but not for stability of the mitochondrial COX1 mRNA in yeast.

21 January 2018

1 reference

Human Mitochondrial mRNAs Are Stabilized with Polyadenylation Regulated by Mitochondria-specific Poly(A) Polymerase and Polynucleotide Phosphorylase

21 January 2018

1 reference

A Novel Modified Nucleoside Found at the First Position of the Anticodon of Methionine tRNA from Bovine Liver Mitochondria

21 January 2018

1 reference